CRANIAL NEUROPATHY ASSOCIATED WITH PRIMARY AMYLOIDOSIS

被引:39
作者
TRAYNOR, AE [1 ]
GERTZ, MA [1 ]
KYLE, RA [1 ]
机构
[1] MAYO CLIN & MAYO FDN,DIV HEMATOL & INTERNAL MED,200 1ST ST,ROCHESTER,MN 55905
关键词
D O I
10.1002/ana.410290421
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report 6 patients for whom cranial neuropathy was a major manifestation of primary amyloidosis. In 3 of the 6, multiple cranial nerves were involved. All had tissue biopsy documentation of amyloidosis. In 2, nerve biopsy also confirmed amyloidosis. All had renal involvement manifested by proteinuria. Primary systemic amyloidosis must be considered in the differential diagnosis of cranial neuropathy, especially when proteinuria is present.
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页码:451 / 454
页数:4
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