EVALUATION OF ROLE OF 5-PHOSPHORIBOSYL-ALPHA-1-PYROPHOSPHATE SYNTHETASE IN CONGENITAL HYPERURICEMIA AND GOUT - SIMPLE ISOTOPIC ASSAY AND AN ACTIVITY STAIN FOR ENZYME

被引:15
作者
JOHNSON, MG
ROSENZWEIG, S
SWITZER, RL
BECKER, MA
SEEGMILLER, JE
机构
[1] UNIV ILLINOIS, DEPT BIOCHEM, URBANA, IL 61801 USA
[2] UNIV CALIF, SAN DIEGO, DEPT MED, LA JOLLA, CA 92037 USA
来源
BIOCHEMICAL MEDICINE | 1974年 / 10卷 / 03期
关键词
D O I
10.1016/0006-2944(74)90030-1
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:266 / 275
页数:10
相关论文
共 29 条
[1]   HUMAN PHOSPHORIBOSYLPYROPHOSPHATE SYNTHETASE - INCREASED ENZYME SPECIFIC ACTIVITY IN A FAMILY WITH GOUT AND EXCESSIVE PURINE SYNTHESIS [J].
BECKER, MA ;
KOSTEL, PJ ;
MEYER, LJ ;
SEEGMILLER, JE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1973, 70 (10) :2749-2752
[2]   PURINE OVERPRODUCTION IN MAN ASSOCIATED WITH INCREASED PHOSPHORIBOSYLPYROPHOSPHATE SYNTHETASE-ACTIVITY [J].
BECKER, MA ;
MEYER, LJ ;
WOOD, AW ;
SEEGMILLER, JE .
SCIENCE, 1973, 179 (4078) :1123-1126
[3]  
CASKEY CT, 1964, J BIOL CHEM, V239, P2570
[4]  
FOX IH, 1971, J BIOL CHEM, V246, P5739
[5]   PHOSPHORIBOSYLPYROPHOSPHATE IN MAN - BIOCHEMICAL AND CLINICAL SIGNIFICANCE [J].
FOX, IH ;
KELLEY, WN .
ANNALS OF INTERNAL MEDICINE, 1971, 74 (03) :424-+
[6]   SIMPLE METHOD FOR PREPARATION OF 32P-LABELLED ADENOSINE TRIPHOSPHATE OF HIGH SPECIFIC ACTIVITY [J].
GLYNN, IM ;
CHAPPELL, JB .
BIOCHEMICAL JOURNAL, 1964, 90 (01) :147-&
[7]  
GREENE ML, 1969, ARTHRITIS RHEUM, V12, P666
[8]  
HENDERSO.JF, 1965, J BIOL CHEM, V240, P2349
[9]  
HERSHKO A, 1968, ISRAEL J MED SCI, V4, P939
[10]   REGULATION OF SYNTHESIS OF 5-PHOSPHORIBOSYL-I-PYROPHOSPHATE IN INTACT RED BLOOD CELLS AND IN CELL-FREE PREPARATIONS [J].
HERSHKO, A ;
RAZIN, A ;
MAGER, J .
BIOCHIMICA ET BIOPHYSICA ACTA, 1969, 184 (01) :64-&