CARNITINE DEFICIENCY WITH VALPROATE THERAPY

被引:17
作者
STUMPF, DA
PARKER, WD
HAAS, R
机构
[1] UNIV COLORADO, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
[2] UNIV CALIF SAN DIEGO, SCH MED, DEPT NEUROL, LA JOLLA, CA 92103 USA
[3] UNIV CALIF SAN DIEGO, SCH MED, DEPT PEDIAT, LA JOLLA, CA 92103 USA
关键词
D O I
10.1016/S0022-3476(83)80831-2
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:175 / 176
页数:2
相关论文
共 6 条
[1]   A MECHANISM OF TOXICITY OF ISOVALERIC ACID IN RAT-LIVER MITOCHONDRIA [J].
BERGEN, BJ ;
STUMPF, DA ;
HAAS, R ;
PARKS, JK ;
EGUREN, LA .
BIOCHEMICAL MEDICINE, 1982, 27 (02) :154-160
[2]   ASSAY OF SHORT-CHAIN ACYL COENZYME-A INTERMEDIATES IN TISSUE-EXTRACTS BY HIGH-PRESSURE LIQUID-CHROMATOGRAPHY [J].
CORKEY, BE ;
BRANDT, M ;
WILLIAMS, RJ ;
WILLIAMSON, JR .
ANALYTICAL BIOCHEMISTRY, 1981, 118 (01) :30-41
[3]   INHIBITORY EFFECTS OF SODIUM VALPROATE ON OXIDATIVE-PHOSPHORYLATION [J].
HAAS, R ;
STUMPF, DA ;
PARKS, JK .
NEUROLOGY, 1981, 31 (11) :1473-1476
[4]   CARNITINE DEFICIENCY AND HYPERAMMONEMIA ASSOCIATED WITH VALPROIC ACID THERAPY [J].
OHTANI, Y ;
ENDO, F ;
MATSUDA, I .
JOURNAL OF PEDIATRICS, 1982, 101 (05) :782-785
[5]   PROPIONATE INHIBITION OF SUCCINATE - COA LIGASE (GDP) AND THE CITRIC-ACID CYCLE IN MITOCHONDRIA [J].
STUMPF, DA ;
MCAFEE, J ;
PARKS, JK ;
EGUREN, L .
PEDIATRIC RESEARCH, 1980, 14 (10) :1127-1131
[6]   UREA CYCLE REGULATION .1. COUPLING OF ORNITHINE METABOLISM TO MITOCHONDRIAL OXIDATIVE-PHOSPHORYLATION [J].
STUMPF, DA ;
PARKS, JK .
NEUROLOGY, 1980, 30 (02) :178-183