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BETA-METHYLCROTONIC ACIDURIA ASSOCIATED WITH LACTIC ACIDOSIS
被引:46
作者
:
ROTH, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
ROTH, K
COHN, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
COHN, R
YANDRASITZ, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
YANDRASITZ, J
PRETI, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
PRETI, G
DODD, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
DODD, P
SEGAL, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
SEGAL, S
机构
:
[1]
UNIV PENN, MONEL CHEM SENSES CTR, PHILADELPHIA, PA USA
[2]
CHILDRENS HOSP, DIV BIOCHEM DEV, PHILADELPHIA, PA 19104 USA
[3]
UNIV PENN, DEPT PEDIAT, PHILADELPHIA, PA USA
[4]
UNIV PENN, DEPT MED, PHILADELPHIA, PA USA
来源
:
JOURNAL OF PEDIATRICS
|
1976年
/ 88卷
/ 02期
关键词
:
D O I
:
10.1016/S0022-3476(76)80987-0
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:229 / 235
页数:7
相关论文
共 23 条
[1]
METHOD FOR DETERMINATION OF VOLATILE ORGANIC-ACIDS IN AQUEOUS-SOLUTIONS AND URINE, AND RESULTS OBTAINED IN PROPIONIC ACIDEMIA, BETA-METHYLCROTONYLGLYCINURIA AND METHYLMALONIC ACIDURIA
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
CHALMERS, RA
BICKLE, S
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
BICKLE, S
WATTS, RWE
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
WATTS, RWE
[J].
CLINICA CHIMICA ACTA,
1974,
52
(01)
: 31
-
41
[2]
QUANTITATIVE EXTRACTION AND GAS-LIQUID CHROMATOGRAPHIC DETERMINATION OF ORGANIC ACIDS IN URINE
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
CLIN RES CTR,MRC,DIV INHERITED METAB DIS,HARROW HA13U,MIDDLESEX,ENGLAND
CLIN RES CTR,MRC,DIV INHERITED METAB DIS,HARROW HA13U,MIDDLESEX,ENGLAND
CHALMERS, RA
[J].
ANALYST,
1972,
97
(1161)
: 958
-
967
[3]
STUDIES ON URINARY ACIDIC METABOLITES EXCRETED BY PATIENTS WITH BETA-METHYLCROTONYLGLYCINURIA, PROPIONIC ACIDEMIA AND METHYLMALONIC ACIDEMIA, USING GAS-LIQUID-CHROMATOGRAPHY AND MASS-SPECTROMETRY
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
CHALMERS, RA
LAWSON, AM
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
LAWSON, AM
WATTS, RWE
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
WATTS, RWE
[J].
CLINICA CHIMICA ACTA,
1974,
52
(01)
: 43
-
51
[4]
ELDJARN L, 1970, LANCET, V2, P521
[5]
CHILD WITH A DEFECT IN LEUCINE METABOLISM ASSOCIATED WITH BETA-HYDROXYISOVALERIC ACIDURIA AND BETA-METHYLCROTONYLGLYCINURIA
GOMPERTZ, D
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
GOMPERTZ, D
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
BARTLETT, K
BLAIR, D
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
BLAIR, D
STERN, CMM
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
STERN, CMM
[J].
ARCHIVES OF DISEASE IN CHILDHOOD,
1973,
48
(12)
: 975
-
977
[6]
GOMPERTZ D, 1971, LANCET, V2, P22
[7]
EVIDENCE FOR ENZYMIC DEFECT IN BETA-METHYLCROTONYLGLYCINURIA
GOMPERTZ, D
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
GOMPERTZ, D
GOODEY, PA
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
GOODEY, PA
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
BARTLETT, K
[J].
FEBS LETTERS,
1973,
32
(01)
: 13
-
14
[8]
HENRY RJ, 1964, CLINICAL CHEMISTRY P
[9]
ABNORMAL RESTING BLOOD LACTATE .1. SIGNIFICANCE OF HYPERLACTATEMIA IN HOSPITALIZED PATIENTS
HUCKABEE, WE
论文数:
0
引用数:
0
h-index:
0
HUCKABEE, WE
[J].
AMERICAN JOURNAL OF MEDICINE,
1961,
30
(06)
: 833
-
&
[10]
DISSEMINATED INTRAVASCULAR COAGULATION
KWAAN, HC
论文数:
0
引用数:
0
h-index:
0
KWAAN, HC
[J].
MEDICAL CLINICS OF NORTH AMERICA,
1972,
56
(01)
: 177
-
+
←
1
2
3
→
共 23 条
[1]
METHOD FOR DETERMINATION OF VOLATILE ORGANIC-ACIDS IN AQUEOUS-SOLUTIONS AND URINE, AND RESULTS OBTAINED IN PROPIONIC ACIDEMIA, BETA-METHYLCROTONYLGLYCINURIA AND METHYLMALONIC ACIDURIA
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
CHALMERS, RA
BICKLE, S
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
BICKLE, S
WATTS, RWE
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
WATTS, RWE
[J].
CLINICA CHIMICA ACTA,
1974,
52
(01)
: 31
-
41
[2]
QUANTITATIVE EXTRACTION AND GAS-LIQUID CHROMATOGRAPHIC DETERMINATION OF ORGANIC ACIDS IN URINE
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
CLIN RES CTR,MRC,DIV INHERITED METAB DIS,HARROW HA13U,MIDDLESEX,ENGLAND
CLIN RES CTR,MRC,DIV INHERITED METAB DIS,HARROW HA13U,MIDDLESEX,ENGLAND
CHALMERS, RA
[J].
ANALYST,
1972,
97
(1161)
: 958
-
967
[3]
STUDIES ON URINARY ACIDIC METABOLITES EXCRETED BY PATIENTS WITH BETA-METHYLCROTONYLGLYCINURIA, PROPIONIC ACIDEMIA AND METHYLMALONIC ACIDEMIA, USING GAS-LIQUID-CHROMATOGRAPHY AND MASS-SPECTROMETRY
CHALMERS, RA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
CHALMERS, RA
LAWSON, AM
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
LAWSON, AM
WATTS, RWE
论文数:
0
引用数:
0
h-index:
0
机构:
MRC,CLIN RES CTR,DIV INHERITED METAB DIS,WATFORD RD,HARROW HA1 3UJ,MIDDLESEX,ENGLAND
WATTS, RWE
[J].
CLINICA CHIMICA ACTA,
1974,
52
(01)
: 43
-
51
[4]
ELDJARN L, 1970, LANCET, V2, P521
[5]
CHILD WITH A DEFECT IN LEUCINE METABOLISM ASSOCIATED WITH BETA-HYDROXYISOVALERIC ACIDURIA AND BETA-METHYLCROTONYLGLYCINURIA
GOMPERTZ, D
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
GOMPERTZ, D
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
BARTLETT, K
BLAIR, D
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
BLAIR, D
STERN, CMM
论文数:
0
引用数:
0
h-index:
0
机构:
HAMMERSMITH HOSP,INST CHILD HLTH,LONDON,ENGLAND
STERN, CMM
[J].
ARCHIVES OF DISEASE IN CHILDHOOD,
1973,
48
(12)
: 975
-
977
[6]
GOMPERTZ D, 1971, LANCET, V2, P22
[7]
EVIDENCE FOR ENZYMIC DEFECT IN BETA-METHYLCROTONYLGLYCINURIA
GOMPERTZ, D
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
GOMPERTZ, D
GOODEY, PA
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
GOODEY, PA
BARTLETT, K
论文数:
0
引用数:
0
h-index:
0
机构:
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
ROY POSTGRAD MED SCH,DEPT MED,LONDON W12,ENGLAND
BARTLETT, K
[J].
FEBS LETTERS,
1973,
32
(01)
: 13
-
14
[8]
HENRY RJ, 1964, CLINICAL CHEMISTRY P
[9]
ABNORMAL RESTING BLOOD LACTATE .1. SIGNIFICANCE OF HYPERLACTATEMIA IN HOSPITALIZED PATIENTS
HUCKABEE, WE
论文数:
0
引用数:
0
h-index:
0
HUCKABEE, WE
[J].
AMERICAN JOURNAL OF MEDICINE,
1961,
30
(06)
: 833
-
&
[10]
DISSEMINATED INTRAVASCULAR COAGULATION
KWAAN, HC
论文数:
0
引用数:
0
h-index:
0
KWAAN, HC
[J].
MEDICAL CLINICS OF NORTH AMERICA,
1972,
56
(01)
: 177
-
+
←
1
2
3
→