DIETARY TREATMENT OF A CHILD WITH MAPLE SYRUP URINE DISEASE (BRANCHED-CHAIN KETOACIDURIA)

被引：77

作者：

WESTALL, RG

机构：

来源：

ARCHIVES OF DISEASE IN CHILDHOOD | 1963年 / 38卷 / 201期

关键词：

D O I：

10.1136/adc.38.201.485

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：485 / +

页数：1

共 14 条

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[2] MAPLE SYRUP URINE DISEASE [J].

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MILLER, S ;

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[3] STUDIES IN MAPLE SYRUP URINE DISEASE [J].

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ARCHIVES OF DISEASE IN CHILDHOOD, 1961, 36 (187) :259-+

[4] STUDIES ON THE METABOLISM OF AMINO ACIDS AND RELATED COMPOUNDS INVIVO .1. TOXICITY OF ESSENTIAL AMINO ACIDS, INDIVIDUALLY AND IN MIXTURES, AND THE PROTECTIVE EFFECT OF L-ARGININE [J].

GULLINO, P ;

WINITZ, M ;

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OTEY, MC ;

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[5]

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[6] A defect in the metabolism of tyrosine and phenylalanine in premature infants. II. Spontaneous occurrence and eradication by vitamin C [J].

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Gordon, Harry H. ;

Marples, Eleanor .

JOURNAL OF CLINICAL INVESTIGATION, 1941, 20 (02) :209-219

[7] MAPLE SYRUP URINE DISEASE - AN INBORN ERROR OF THE METABOLISM OF VALINE, LEUCINE, AND ISOLEUCINE ASSOCIATED WITH GROSS MENTAL DEFICIENCY [J].

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WOOLF, LI .

BRITISH MEDICAL JOURNAL, 1959, 1 (JAN10) :90-91

[8]

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[9]

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[10]

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