GLYCOSYLCERAMIDE SYNTHESIS IN THE DEVELOPING SPINAL-CORD AND KIDNEY OF THE TWITCHER MOUSE, AN ENZYMATICALLY AUTHENTIC MODEL OF HUMAN KRABBE DISEASE

被引:32
作者
KODAMA, S
IGISU, H
SIEGEL, DA
SUZUKI, K
机构
[1] YESHIVA UNIV ALBERT EINSTEIN COLL MED,ROSE F KENNEDY CTR RES MENTAL RETARDAT & HUMAN DEV,BRONX,NY 10461
[2] YESHIVA UNIV ALBERT EINSTEIN COLL MED,SAUL R KOREY DEPT NEUROL,BRONX,NY 10461
[3] YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT NEUROSCI,BRONX,NY 10461
关键词
D O I
10.1111/j.1471-4159.1982.tb12572.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1314 / 1318
页数:5
相关论文
共 26 条
[1]   SYNTHESIS OF GALACTOSYL CERAMIDE AND GLUCOSYL CERAMIDE BY RAT-BRAIN - ASSAY PROCEDURES AND CHANGES WITH AGE [J].
BRENKERT, A ;
RADIN, NS .
BRAIN RESEARCH, 1972, 36 (01) :183-&
[2]   USE OF LIPOSOMES AS ACCEPTORS FOR THE ASSAY OF LIPID GLYCOSYLTRANSFERASES FROM RAT-BRAIN [J].
CESTELLI, A ;
WHITE, FV ;
COSTANTINOCECCARINI, E .
BIOCHIMICA ET BIOPHYSICA ACTA, 1979, 572 (02) :283-292
[3]  
COSTANTI.E, 1973, J BIOL CHEM, V248, P8240
[4]  
COSTANTINOCECCA.E, 1976, CURRENT TRENDS SPHIN, P127
[5]   HEPATIC GALACTOSYLCERAMIDE IN GLOBOID-CELL LEUKODYSTROPHY (KRABBES DISEASE) [J].
DAWSON, G .
LIPIDS, 1973, 8 (03) :154-156
[6]   HEREDITARY LEUCODYSTROPHY IN THE MOUSE - THE NEW MUTANT TWITCHER [J].
DUCHEN, LW ;
EICHER, EM ;
JACOBS, JM ;
SCARAVILLI, F ;
TEIXEIRA, F .
BRAIN, 1980, 103 (SEP) :695-710
[8]   THE TWITCHER MOUSE - DETERMINATION OF GENETIC STATUS BY GALACTOSYLCERAMIDASE ASSAYS ON CLIPPED TAIL [J].
KOBAYASHI, T ;
NAGARA, H ;
SUZUKI, K ;
SUZUKI, K .
BIOCHEMICAL MEDICINE, 1982, 27 (01) :8-14
[9]   THE TWITCHER MOUSE - AN ENZYMATICALLY AUTHENTIC MODEL OF HUMAN GLOBOID-CELL LEUKODYSTROPHY (KRABBE DISEASE) [J].
KOBAYASHI, T ;
YAMANAKA, T ;
JACOBS, JM ;
TEIXEIRA, F ;
SUZUKI, K .
BRAIN RESEARCH, 1980, 202 (02) :479-483
[10]  
KOBAYASHI T, 1980, NEUROLOGICAL MUTATIO, P253