THE EFFECT OF A HIGH PROTEIN-DIET ON LEUCINE AND ALANINE TURNOVER IN ACID MALTASE DEFICIENCY

被引:17
作者
UMPLEBY, AM
STJTREND, P
CHUBB, D
CONAGLEN, JV
WILLIAMS, CD
HESP, R
SCOBIE, IN
WILES, CM
SPENCER, G
SONKSEN, PH
机构
[1] UNIV MED & DENT SCH GUYS & ST THOMAS HOSP,RESP UNIT,LONDON SE1 7EH,ENGLAND
[2] UNIV MED & DENT SCH GUYS & ST THOMAS HOSP,DEPT NEUROL,LONDON SE1 7EH,ENGLAND
[3] CLIN RES CTR,MRC,DIV RADIOISOTOPES,HARROW HA1 3UJ,MIDDX,ENGLAND
关键词
D O I
10.1136/jnnp.52.8.954
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:954 / 961
页数:8
相关论文
共 36 条
[1]   ABDOMINAL AND THORACIC PRESSURES AT DIFFERENT LUNG VOLUMES [J].
AGOSTONI, E ;
RAHN, H .
JOURNAL OF APPLIED PHYSIOLOGY, 1960, 15 (06) :1087-1092
[2]   COMPARATIVE STUDY OF ACID MALTASE DEFICIENCY - BIOCHEMICAL DIFFERENCES BETWEEN INFANTILE, CHILDHOOD, AND ADULT TYPES [J].
ANGELINI, C ;
ENGEL, AG .
ARCHIVES OF NEUROLOGY, 1972, 26 (04) :344-+
[3]   ADULT ACID MALTASE DEFICIENCY - ABNORMALITIES IN FIBROBLASTS CULTURED FROM PATIENTS [J].
ANGELINI, C ;
TITUS, JL ;
ENGEL, AG .
NEW ENGLAND JOURNAL OF MEDICINE, 1972, 287 (19) :948-&
[4]  
BIRKHAHN RH, 1980, SURGERY, V88, P294
[5]  
BJORNTONP P, 1977, DIABETES, V22, P238
[6]  
BLACK LF, 1971, AM REV RESPIR DIS, V103, P641
[7]   RELATION OF TOTAL-BODY POTASSIUM TO HEIGHT, WEIGHT, AND AGE IN NORMAL ADULTS [J].
BODDY, K ;
HUME, R ;
WEYERS, E ;
KING, PC .
JOURNAL OF CLINICAL PATHOLOGY, 1972, 25 (06) :512-&
[8]   FREE FATTY-ACID ESTIMATION BY A SEMIAUTOMATED FLUORIMETRIC METHOD [J].
CARRUTHERS, M ;
YOUNG, DAB .
CLINICA CHIMICA ACTA, 1973, 49 (03) :341-348
[9]  
DIMAURO S, 1980, HDB CLIN NEUROLOGY, V41, P174
[10]  
DOLE VP, 1960, J BIOL CHEM, V235, P2595