CHARACTERIZATION OF CELLULAR OLIGOSACCHARIDES FROM NORMAL AND CYSTIC FIBROTIC FIBROBLASTS USING SEQUENTIAL ENDOGLYCOSIDASE DIGESTIONS

被引:15
作者
BOZON, D [1 ]
TARENTINO, AL [1 ]
TRIMBLE, RB [1 ]
MALEY, F [1 ]
机构
[1] NEW YORK STATE DEPT HLTH,WADSWORTH CTR LABS & RES,EMPIRE STATE PLAZA,ALBANY,NY 12201
关键词
D O I
10.1016/0003-9861(86)90032-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:546 / 556
页数:11
相关论文
共 21 条
[1]  
ARUMUGHAM RG, 1983, J BIOL CHEM, V258, P1883
[2]  
BYRD JC, 1982, J BIOL CHEM, V257, P4657
[3]   STRUCTURE OF THE LIPID-LINKED OLIGOSACCHARIDES THAT ACCUMULATE IN CLASS-E THY-1-NEGATIVE MUTANT LYMPHOMAS [J].
CHAPMAN, A ;
TROWBRIDGE, IS ;
HYMAN, R ;
KORNFELD, S .
CELL, 1979, 17 (03) :509-515
[4]  
ELBEIN AD, 1981, P NATL ACAD SCI-BIOL, V78, P7393, DOI 10.1073/pnas.78.12.7393
[5]   CYSTIC-FIBROSIS - DECREASED THERMOSTABILITY OF ALPHA-MANNOSIDASE IN CRUDE EXTRACELLULAR FLUIDS OF PATIENTS AND CARRIERS [J].
HOSLI, P ;
VOGT, E .
FEBS LETTERS, 1979, 104 (02) :271-274
[6]   CYSTIC-FIBROSIS - LEAKAGE OF LYSOSOMAL ENZYMES AND OF ALKALINE-PHOSPHATASE INTO EXTRACELLULAR-SPACE [J].
HOSLI, P ;
VOGT, E .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 79 (03) :741-748
[7]  
MALER T, 1981, J BIOL CHEM, V256, P1420
[8]   ENHANCED UDP-GALACTOSE - GLYCOPROTEIN GALACTOSYL TRANSFERASE-ACTIVITY IN CULTIVATED SKIN FIBROBLASTS FROM PATIENTS WITH CYSTIC-FIBROSIS AND ITS POSSIBLE RELATIONSHIP TO PATHOGENESIS OF DISEASE [J].
RAO, GJS ;
SPELLS, G ;
NADLER, HL .
PEDIATRIC RESEARCH, 1977, 11 (09) :981-985
[9]   ABNORMAL DISTRIBUTION OF ALPHA-L-FUCOSIDASE IN CYSTIC-FIBROSIS - INCREASED ACTIVITY IN SKIN FIBROBLASTS [J].
SCANLIN, TF ;
MATACIC, SS ;
PACE, M ;
SANTER, UV ;
GLICK, MC .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 79 (03) :869-875
[10]  
SCANLIN TF, 1982, BIOCHEMISTRY, V3, P491