TREATMENT OF CARBAMYL-PHOSPHATE SYNTHETASE DEFICIENCY WITH KETO ANALOGUES OF ESSENTIAL AMINO-ACIDS

被引：96

作者：

BATSHAW, M

BRUSILOW, S

WALSER, M

机构：

[1] JOHNS HOPKINS HOSP,JOHN F KENNEDY INST,DEPT MED,BALTIMORE,MD 21205

[2] JOHNS HOPKINS HOSP,JOHN F KENNEDY INST,DEPT PHARMACOL & EXPTL THERAPEUTICS,BALTIMORE,MD 21205

[3] JOHNS HOPKINS HOSP,JOHN F KENNEDY INST,DEPT PEDIAT,BALTIMORE,MD 21205

[4] JOHNS HOPKINS UNIV,SCH MED,DEPT PHARMACOL,BALTIMORE,MD 21205

来源：

NEW ENGLAND JOURNAL OF MEDICINE | 1975年 / 292卷 / 21期

关键词：

D O I：

10.1056/NEJM197505222922101

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

收藏

页码：1085 / 1090

页数：6

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