THE ACOUSTIC STARTLE REFLEX IN STIFF-MAN SYNDROME

被引:35
作者
MATSUMOTO, JY [1 ]
CAVINESS, JN [1 ]
MCEVOY, KM [1 ]
机构
[1] MAYO CLIN SCOTTSDALE,DEPT NEUROL,SCOTTSDALE,AZ
关键词
D O I
10.1212/WNL.44.10.1952
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We studied the EMG response to loud noise in eight patients with stiff-man syndrome (SMS). Audiogenic muscle jerks originated in the acoustic startle reflex. Patients demonstrated excessive, poorly habituating motor activity predominately in axial and leg muscles. Exaggerated startle in SMS probably reflects segmental hyperexcitability of axial and lumbar spinal motor neurons.
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收藏
页码:1952 / 1955
页数:4
相关论文
共 10 条
[1]   THE HYPEREKPLEXIAS AND THEIR RELATIONSHIP TO THE NORMAL STARTLE REFLEX [J].
BROWN, P ;
ROTHWELL, JC ;
THOMPSON, PD ;
BRITTON, TC ;
DAY, BL ;
MARSDEN, CD .
BRAIN, 1991, 114 :1903-1928
[2]   NEW OBSERVATIONS ON THE NORMAL AUDITORY STARTLE REFLEX IN MAN [J].
BROWN, P ;
ROTHWELL, JC ;
THOMPSON, PD ;
BRITTON, TC ;
DAY, BL ;
MARSDEN, CD .
BRAIN, 1991, 114 :1891-1902
[3]   HUMAN STARTLE REFLEX - TECHNIQUE AND CRITERIA FOR ABNORMAL RESPONSE [J].
CHOKROVERTY, S ;
WALCZAK, T ;
HENING, W .
ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1992, 85 (04) :236-242
[4]  
DAVIS M, 1982, J NEUROSCI, V2, P791
[5]   PHYSIOLOGICAL ABNORMALITIES IN HEREDITARY HYPEREKPLEXIA [J].
MATSUMOTO, J ;
FUHR, P ;
NIGRO, M ;
HALLETT, M .
ANNALS OF NEUROLOGY, 1992, 32 (01) :41-50
[6]   NEUROPHARMACOLOGICAL INVESTIGATIONS IN THE STIFF-MAN SYNDROME [J].
MEINCK, HM ;
CONRAD, B .
JOURNAL OF NEUROLOGY, 1986, 233 (06) :340-347
[7]   SUDDEN-DEATH AND PAROXYSMAL AUTONOMIC DYSFUNCTION IN STIFF-MAN SYNDROME [J].
MITSUMOTO, H ;
SCHWARTZMAN, MJ ;
ESTES, ML ;
CHOU, SM ;
LAFRANCHISE, EF ;
DECAMILLI, P ;
SOLIMENA, M .
JOURNAL OF NEUROLOGY, 1991, 238 (02) :91-96
[8]  
MOERSCH FP, 1956, P STAFF M MAYO CLIN, V31, P421
[9]  
ROSSI B, 1988, Electromyography and Clinical Neurophysiology, V28, P137
[10]   AUDIOGENIC STARTLE REFLEX OF MAN AND ITS RELATIONSHIP TO STARTLE SYNDROMES - A REVIEW [J].
WILKINS, DE ;
HALLETT, M ;
WESS, MM .
BRAIN, 1986, 109 :561-573