PREVALENCE STUDY OF RETT SYNDROME IN NORTH-DAKOTA CHILDREN

被引:17
作者
BURD, L
VESLEY, B
MARTSOLF, JT
KERBESHIAN, J
机构
[1] UNIV N DAKOTA,DEPT NEUROSCI,GRAND FORKS,ND 58202
[2] UNIV N DAKOTA,DEPT PEDIAT,DIV MED GENET,GRAND FORKS,ND 58202
来源
AMERICAN JOURNAL OF MEDICAL GENETICS | 1991年 / 38卷 / 04期
关键词
PREVALENCE; EPIDEMIOLOGY; CHILDREN; NORTH-DAKOTA; MENTAL RETARDATION;
D O I
10.1002/ajmg.1320380414
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
Service providers for children in the state of North Dakota were surveyed to determine the prevalence rate of Rett syndrome (RS). Five patients with definite RS were identified in a population of 203,801 children (98,932 girls) 0-18 years of age yielding a prevalence rate of RS of 1 in 40,760 in North Dakota children. For girls the rate of RS is 1 in 19,786. Similar surveys of other states using comparable modes of ascertainment will be important as points of comparison for prevalence rates of RS.
引用
收藏
页码:565 / 568
页数:4
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