COMPLEMENT PROFILE IN A CI INHIBITOR DEFICIENT FAMILY

被引:6
作者
SAYAMA, K
SHIRAISHI, S
MIKI, Y
机构
关键词
D O I
10.1111/j.1365-2133.1985.tb02410.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
收藏
页码:737 / 743
页数:7
相关论文
共 18 条
[1]   REACTION MECHANISM OF HUMAN C5 IN IMMUNE HEMOLYSIS [J].
COOPER, NR ;
MULLEREB.HJ .
JOURNAL OF EXPERIMENTAL MEDICINE, 1970, 132 (04) :775-&
[2]   A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE [J].
DONALDSON, VH ;
EVANS, RR .
AMERICAN JOURNAL OF MEDICINE, 1963, 35 (01) :37-+
[3]   LUPUS-ERYTHEMATOSUS-LIKE DISEASE IN 3 UNRELATED WOMEN WITH HEREDITARY ANGIONEUROTIC-EDEMA [J].
DONALDSON, VH ;
HESS, EV ;
MCADAMS, AJ .
ANNALS OF INTERNAL MEDICINE, 1977, 86 (03) :312-313
[4]   PERMEABILITY-INCREASING ACTIVITY IN HEREDITARY ANGIONEUROTIC EDEMA PLASMA .2. MECHANISM OF FORMATION AND PARTIAL CHARACTERIZATION [J].
DONALDSON, VH ;
RATNOFF, OD ;
DASILVA, WD ;
ROSEN, FS .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (04) :642-+
[5]   RESPONSE OF VARIANT HEREDITARY ANGIOEDEMA PHENOTYPES TO DANAZOL THERAPY - GENETIC-IMPLICATIONS [J].
GADEK, JE ;
HOSEA, SW ;
GELFAND, JA ;
FRANK, MM .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (01) :280-286
[6]  
GAITHER TA, 1974, J IMMUNOL, V113, P574
[7]   TREATMENT OF HEREDITARY ANGIOEDEMA WITH DANAZOL - REVERSAL OF CLINICAL AND BIOCHEMICAL ABNORMALITIES [J].
GELFAND, JA ;
SHERINS, RJ ;
ALLING, DW ;
FRANK, MM .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 295 (26) :1444-1448
[8]  
Hugli T E, 1978, Adv Immunol, V26, P1, DOI 10.1016/S0065-2776(08)60228-X
[9]   THE ACTIVE-SITE OF HUMAN C4A ANAPHYLATOXIN [J].
HUGLI, TE ;
KAWAHARA, MS ;
UNSON, CG ;
MOLINARRODE, R ;
ERICKSON, BW .
MOLECULAR IMMUNOLOGY, 1983, 20 (06) :637-645
[10]   C1 INHIBITOR - EVIDENCE FOR DECREASED HEPATIC SYNTHESIS IN HEREDITARY ANGIONEUROTIC EDEMA [J].
JOHNSON, AM ;
ALPER, CA ;
ROSEN, FS ;
CRAIG, JM .
SCIENCE, 1971, 173 (3996) :553-&