TRANSIENT OVERMODIFICATION OF COLLAGEN-I AND III IN A HYPERPLASTIC CALLUS FROM A PATIENT WITH OSTEOGENESIS IMPERFECTA TYPE-IV

被引:3
作者
BRENNER, RE
LEHMANN, H
NOTBOHM, H
NERLICH, A
VETTER, U
MULLER, PK
机构
[1] UNIV LUBECK,INST MED MOLEK BIOL,RATZEBURGER ALLEE 160,W-24000 LUBECK,GERMANY
[2] UNIV MUNICH,INST PATHOL,W-8000 MUNICH 70,GERMANY
[3] NIH,BETHESDA,MD 20892
关键词
D O I
10.1111/j.1749-6632.1990.tb17987.x
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
[No abstract available]
引用
收藏
页码:549 / 551
页数:3
相关论文
共 6 条
[1]  
BYERS PH, 1988, AM J HUM GENET, V42, P237
[2]   COLLAGEN GENES AND INHERITED CONNECTIVE-TISSUE DISEASE [J].
CHEAH, KSE .
BIOCHEMICAL JOURNAL, 1985, 229 (02) :287-303
[3]   DISORDER OF COLLAGEN-METABOLISM IN A PATIENT WITH OSTEOGENESIS IMPERFECTA (LETHAL TYPE) - INCREASED DEGREE OF HYDROXYLATION OF LYSINE IN COLLAGEN TYPE-I AND TYPE-III [J].
KIRSCH, E ;
KRIEG, T ;
REMBERGER, K ;
FENDEL, H ;
BRUCKNER, P ;
MULLER, PK .
EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, 1981, 11 (01) :39-47
[4]  
PROCKOP DJ, 1986, RHEUMATOLOGY, V10, P246
[5]   GENETIC-HETEROGENEITY IN OSTEOGENESIS IMPERFECTA [J].
SILLENCE, DO ;
SENN, A ;
DANKS, DM .
JOURNAL OF MEDICAL GENETICS, 1979, 16 (02) :101-116
[6]   HYPERPLASTIC CALLUS FORMATION IN OSTEOGENESIS IMPERFECTA - REPORT OF A CASE AND REVIEW OF THE LITERATURE [J].
STRACH, EH .
JOURNAL OF BONE AND JOINT SURGERY-BRITISH VOLUME, 1953, 35 (03) :417-422