NIEMANN-PICK VARIANT DISORDERS - COMPARISON OF ERRORS OF CELLULAR CHOLESTEROL HOMEOSTASIS IN GROUP-D AND GROUP-C FIBROBLASTS

被引:39
作者
BUTLER, JD
COMLY, ME
KRUTH, HS
VANIER, M
FILLINGKATZ, M
FINK, J
BARTON, N
WEINTROUB, H
QUIRK, JM
TOKORO, T
MARSHALL, DC
BRADY, RO
PENTCHEV, PG
机构
[1] NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20892
[2] NHLBI,EXPTL ATHEROSCLEROSIS LAB,BETHESDA,MD 20892
[3] FAC MED LYON SUD,BIOCHIM LAB,INSERM,U189,F-69921 OULLINS,FRANCE
[4] TEL AVIV UNIV,SACKLER SCH MED,DEV PATHOL LAB,IL-69978 TEL AVIV,ISRAEL
关键词
D O I
10.1073/pnas.84.2.556
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:556 / 560
页数:5
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