NEUROLYMPHOMATOSIS - A CLINICOPATHOLOGICAL SYNDROME REEMERGES

被引:74
作者
DIAZARRASTIA, R
YOUNGER, DS
HAIR, L
INGHIRAMI, G
HAYS, AP
KNOWLES, DM
ODEL, JG
FETELL, MR
LOVELACE, RE
ROWLAND, LP
机构
[1] COLUMBIA PRESBYTERIAN MED CTR, DEPT NEUROL, 710 W 168TH ST, BOX 53, NEW YORK, NY 10032 USA
[2] COLUMBIA PRESBYTERIAN MED CTR, DEPT PATHOL, NEW YORK, NY 10032 USA
[3] COLUMBIA PRESBYTERIAN MED CTR, DEPT OPHTHALMOL, NEW YORK, NY 10032 USA
关键词
D O I
10.1212/WNL.42.6.1136
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe a patient with sensorimotor peripheral neuropathy and cranial neuropathy due to autopsy-proven neurolymphomatosis defined by infiltration of peripheral nerves by tumor cells and review the findings in 39 previously reported patients. The cause of the neuropathy is not known. The association with immune-deficient states suggests virally mediated pathogenesis, possibly a retrovirus.
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页码:1136 / 1141
页数:6
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