FAMILIAL ESSENTIAL THROMBOCYTHEMIA

被引:21
作者
FERNANDEZROBLES, E [1 ]
VERMYLEN, C [1 ]
MARTIAT, P [1 ]
NINANE, J [1 ]
CORNU, G [1 ]
机构
[1] CATHOLIC UNIV LOUVAIN CLIN,DEPT HAEMATOL,B-1200 BRUSSELS,BELGIUM
关键词
Familial thrombocythemia; Myeloproliferative disease;
D O I
10.3109/08880019009033414
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We report three siblings (2 F, 1 M) aged 9, 12, and 15 years with a thrombocytosis, above 650 × 109/l for at least 18 months and a leukocyte alkaline phosphatase score below 37. The diagnosis of essential thrombocythemia was based upon the exclusion of a reactive thrombocytosis or another myeloproliferative disease. Cytogenetic examination of marrow cells was normal. © 1990 Informa UK Ltd All rights reserved: reproduction in whole or part not permitted.
引用
收藏
页码:373 / 376
页数:4
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