ADRENOCORTICOTROPIC HORMONE INSENSITIVITY ASSOCIATED WITH AUTONOMIC NERVOUS-SYSTEM DISORDERS

被引：28

作者：

DUMIC, M ^{[1
]}

RADICA, A ^{[1
]}

SABOL, Z ^{[1
]}

PLAVSIC, V ^{[1
]}

BRKLJACIC, L ^{[1
]}

SARNAVKA, V ^{[1
]}

VUKOVIC, J ^{[1
]}

机构：

[1] UNIV ZAGREB, UNIV HOSP REBRO, CTR TISSUE TYPING, YU-41000 Zagreb, YUGOSLAVIA

来源：

EUROPEAN JOURNAL OF PEDIATRICS | 1991年 / 150卷 / 10期

关键词：

ACTH INSENSITIVITY; ADRENAL INSUFFICIENCY; AUTONOMIC NERVOUS SYSTEM DISORDERS; OSTEOPOROSIS; HLA TYPING;

D O I：

10.1007/BF01958757

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Five children with adrenocorticotropic hormone (ACTH) insensitivity associated with autonomic nervous system disorders are described. At the time of diagnosis, four of them had osteoporosis. The fifth patient died and skeletal roentgenograms were not done. Osteoporosis was subsequently discovered in one of our previously reported patients with ACTH insensitivity. We assume that osteoporosis is, at least partly, the result of decreased adrenal androgen production. Human leucocyte antigen typing failed to establish any linkage.

引用

页码：696 / 699

页数：4

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