STORAGE BODIES IN THE CEROID-LIPOFUSCINOSES (BATTEN-DISEASE) - LOW-MOLECULAR-WEIGHT COMPONENTS, UNUSUAL AMINO-ACIDS AND RECONSTITUTION OF FLUORESCENT BODIES FROM NONFLUORESCENT COMPONENTS

被引：21

作者：

PALMER, DN

BAYLISS, SL

CLIFTON, PA

GRANT, VJ

机构：

[1] Department of Veterinary Pathology and Public Health, Massey University, Palmerston North

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1993年 / 16卷 / 02期

关键词：

D O I：

10.1007/BF00710268

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：292 / 295

页数：4

共 11 条

[1] THE SEQUENCE OF THE MAJOR PROTEIN STORED IN OVINE CEROID LIPOFUSCINOSIS IS IDENTICAL WITH THAT OF THE DICYCLOHEXYLCARBODIIMIDE-REACTIVE PROTEOLIPID OF MITOCHONDRIAL ATP SYNTHASE [J].

FEARNLEY, IM ;

WALKER, JE ;

MARTINUS, RD ;

JOLLY, RD ;

KIRKLAND, KB ;

SHAW, GJ ;

PALMER, DN .

BIOCHEMICAL JOURNAL, 1990, 268 (03) :751-758

[2] SHEEP AND OTHER ANIMALS WITH CEROID-LIPOFUSCINOSES - THEIR RELEVANCE TO BATTEN DISEASE [J].

JOLLY, RD ;

MARTINUS, RD ;

PALMER, DN .

AMERICAN JOURNAL OF MEDICAL GENETICS, 1992, 42 (04) :609-614

[3] STORAGE PROTEIN IN HEREDITARY CEROID-LIPOFUSCINOSIS CONTAINS S-METHYLATED METHIONINE [J].

KATZ, ML ;

GERHARDT, KO .

MECHANISMS OF AGEING AND DEVELOPMENT, 1990, 53 (03) :277-&

[4] METHYLATED LYSINE IN STORAGE BODY PROTEIN OF SHEEP WITH HEREDITARY CEROID-LIPOFUSCINOSIS [J].

KATZ, ML ;

GERHARDT, KO .

BIOCHIMICA ET BIOPHYSICA ACTA, 1992, 1138 (02) :97-108

[5]

KATZ ML, 1991, AM J PATHOL, V138, P323

[6] LOW-MOLECULAR-WEIGHT URINARY PEPTIDES IN CEROID-LIPOFUSCINOSES - POTENTIAL BIOCHEMICAL MARKERS FOR THE JUVENILE SUBTYPE [J].

LABADIE, GU ;

PULLARKAT, RK .

AMERICAN JOURNAL OF MEDICAL GENETICS, 1990, 37 (04) :592-599

[7]

PALMER DN, 1986, J BIOL CHEM, V261, P1766

[8] MITOCHONDRIAL ATP SYNTHASE SUBUNIT C STORAGE IN THE CEROID-LIPOFUSCINOSES (BATTEN DISEASE) [J].

PALMER, DN ;

FEARNLEY, IM ;

WALKER, JE ;

HALL, NA ;

LAKE, BD ;

WOLFE, LS ;

HALTIA, M ;

MARTINUS, RD ;

JOLLY, RD .

AMERICAN JOURNAL OF MEDICAL GENETICS, 1992, 42 (04) :561-567

[9]

PALMER DN, 1989, J BIOL CHEM, V264, P5736

[10]

PALMER DN, 1990, LIPOFUSCIN CEROID PI, P211

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