EMERGENCY OPERATION FOR THORACIC AORTIC-ANEURYSM CAUSED BY THE EHLERS-DANLOS SYNDROME

被引：10

作者：

HAMANO, K

MINAMI, Y

FUJIMURA, Y

TSUBOI, H

FURUKAWA, S

ODA, T

ESATO, K

机构：

[1] First Department of Surgery, Yamaguchi University School of Medicine, Department of Surgery, Yamaguchi

来源：

ANNALS OF THORACIC SURGERY | 1994年 / 58卷 / 04期

关键词：

D O I：

10.1016/0003-4975(94)90488-X

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Two patients were treated emergently for impending ruptured thoracic aortic aneurysms caused by type IV Ehlers-Danlos syndrome. One patient had typical physical evidence of type IV Ehlers-Danlos syndrome. The other patient had a normal phenotype. Type IV Ehlers-Danlos syndrome was diagnosed by electrophoresis of the collagen extracted from the skin. The clinician must be aware of the variations in presentation of type IV Ehlers-Danlos syndrome.

引用

页码：1180 / 1182

页数：3

共 8 条

[1] MOLECULAR-BASIS OF CLINICAL HETEROGENEITY IN THE EHLERS-DANLOS SYNDROME [J].