GLUTARIC ACIDURIA - INHERITED DEFICIENCY OF GLUTARYL-COA DEHYDROGENASE-ACTIVITY

被引:68
作者
GOODMAN, SI
KOHLHOFF, JG
机构
[1] UNIV COLORADO,MED CTR,DEPT PEDIAT,DENVER,CO 80220
[2] UNIV COLORADO,MED CTR,RES BIOCHEM,DENVER,CO
来源
BIOCHEMICAL MEDICINE | 1975年 / 13卷 / 02期
关键词
D O I
10.1016/0006-2944(75)90149-0
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:138 / 140
页数:3
相关论文
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[2]   GLUTARIC ACIDURIA - NEW DISORDER OF AMINO-ACID METABOLISM [J].
GOODMAN, SI ;
MARKEY, SP ;
MOE, PG ;
MILES, BS ;
TENG, CC .
BIOCHEMICAL MEDICINE, 1975, 12 (01) :12-21
[3]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[4]   GLUTARIC ACIDURIA - PRESENCE OF GLUTACONIC AND BETA-HYDROXYGLUTARIC ACIDS IN URINE [J].
STOKKE, O ;
GOODMAN, SI ;
THOMPSON, JA ;
MILES, BS .
BIOCHEMICAL MEDICINE, 1975, 12 (04) :386-391