PANCOLONIC DISEASE IN CYSTIC-FIBROSIS AND HIGH-DOSE PANCREATIC-ENZYME THERAPY

被引:25
作者
PETTEI, MJ
LEONIDAS, JC
LEVINE, JJ
GORVOY, JD
机构
[1] LONG ISL JEWISH MED CTR, SCHNEIDER CHILDRENS HOSP, DIV PEDIAT RADIOL, NEW HYDE PK, NY 11042 USA
[2] LONG ISL JEWISH MED CTR, SCHNEIDER CHILDRENS HOSP, CTR CYST FIBROSIS, NEW HYDE PK, NY 11042 USA
关键词
D O I
10.1016/S0022-3476(94)70014-1
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We describe a child with cystic fibrosis who was treated with high-dose pancreatic enzyme replacement therapy and who had a prominent ascending colon stricture with submucosal fibrosis. Unlike prior reported cases, this patient's disease was more extensive, involving the entire colon, and was associated with chylous ascites.
引用
收藏
页码:587 / 589
页数:3
相关论文
共 8 条
[1]  
CAMPBELL CA, 1994, LANCET, V343, P109
[2]  
CLEGHORN GJ, 1986, LANCET, V1, P8
[3]  
OADES PJ, 1994, LANCET, V343, P109, DOI 10.1016/S0140-6736(94)90836-2
[4]  
OADES PJ, 1992, PEDIATR PULM S, V8, P312
[5]   HIGH-DOSE PANCREATIC-ENZYMES IN CYSTIC-FIBROSIS [J].
ROBINSON, PJ ;
SLY, PD .
ARCHIVES OF DISEASE IN CHILDHOOD, 1990, 65 (03) :311-312
[6]   INCIDENCE OF DISTAL INTESTINAL-OBSTRUCTION SYNDROME IN CYSTIC-FIBROSIS [J].
ROSENSTEIN, BJ ;
LANGBAUM, TS .
JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1983, 2 (02) :299-301
[7]   STRICTURES OF ASCENDING COLON IN CYSTIC-FIBROSIS AND HIGH-STRENGTH PANCREATIC-ENZYMES [J].
SMYTH, RL ;
VANVELZEN, D ;
SMYTH, AR ;
LLOYD, DA ;
HEAF, DP .
LANCET, 1994, 343 (8889) :85-86
[8]   RADIOGRAPHIC ABNORMALITIES OF DUODENUM AND SMALL BOWEL IN CYSTIC-FIBROSIS OF PANCREAS (MUCOVISCIDOSIS) [J].
TAUSSIG, LM ;
SALDINO, RM ;
DISANTAG.PA .
RADIOLOGY, 1973, 106 (02) :369-376