CYSTINE TRANSPORT IS DEFECTIVE IN ISOLATED LEUKOCYTE LYSOSOMES FROM PATIENTS WITH CYSTINOSIS

被引：308

作者：

GAHL, WA ^{[1
]}

BASHAN, N ^{[1
]}

TIETZE, F ^{[1
]}

BERNARDINI, I ^{[1
]}

SCHULMAN, JD ^{[1
]}

机构：

[1] NIADDKD,INTERMEDIARY METAB SECT,BETHESDA,MD 20205

来源：

关键词：

D O I：

10.1126/science.7112129

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：1263 / 1265

页数：3

共 17 条

[1] BASHAN N, UNPUB
[2] GAHL W, UNPUB
[3] GAHL WA, J BIOL CHEM
[4] Geiger B, 1978, Methods Enzymol, V50, P547
[5] RUPTURE OF RAT-LIVER LYSOSOMES MEDIATED BY L-AMINO-ACID ESTERS
GOLDMAN, R
KAPLAN, A
[J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1973, 318 (02) : 205 - 216
[6] CYSTINE ACCUMULATION AND LOSS IN NORMAL, HETEROZYGOUS, AND CYSTINOTIC FIBROBLASTS
JONAS, AJ
GREENE, AA
SMITH, ML
SCHNEIDER, JA
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (14): : 4442 - 4445
[7] LAHRICHI M, 1977, BIOCH BIOPHYS ACTA, V79, P479
[8] OSHIMA RG, 1974, J BIOL CHEM, V249, P6033
[9] REEVES JP, 1979, J BIOL CHEM, V254, P8914
[10] ROME LH, 1981, J BIOL CHEM, V256, P763