THROMBOTIC THROMBOCYTOPENIC PURPURA ASSOCIATED WITH SICKLE CELL-HEMOGLOBIN-C-DISEASE

被引:15
作者
CHINOWSKY, MS
机构
[1] Department of Internal Medicine, Kaiser Permanente Medical Center, Harbor, CA
关键词
D O I
10.1097/00007611-199411000-00025
中图分类号
R5 [内科学];
学科分类号
1002 [临床医学]; 100201 [内科学];
摘要
Thrombotic thrombocytopenic purpura (TTP) complicated a vaso-occlusive crisis in a patient with sickle cell-hemoglobin C (HbSC) disease. Markedly abnormal HbSC red blood cell morphology confused the initial diagnostic evaluation of the peripheral smear. Sustained, severe thrombocytopenia and the patient's failure to respond clinically to RBC exchange transfusion helped to indicate the proper diagnosis that led to effective therapy.
引用
收藏
页码:1168 / 1171
页数:4
相关论文
共 38 条
[1]
SEVERE THROMBOCYTOPENIA IN SICKLE-CELL CRISIS [J].
ALLEN, U ;
MACKINNON, H ;
ZIPURSKY, A ;
STEVENS, M .
PEDIATRIC HEMATOLOGY AND ONCOLOGY, 1988, 5 (02) :137-141
[2]
AMAROSI EL, 1966, MEDICINE, V45, P139
[3]
CLINICAL, HEMATOLOGICAL, AND BIOCHEMICAL FEATURES OF HB SC DISEASE [J].
BALLAS, SK ;
LEWIS, CN ;
NOONE, AM ;
KRASNOW, SH ;
KAMARULZAMAN, E ;
BURKA, ER .
AMERICAN JOURNAL OF HEMATOLOGY, 1982, 13 (01) :37-51
[4]
BARRERAS L, 1968, JAMA-J AM MED ASSOC, V203, P127
[5]
BRITTAIN HA, 1993, BLOOD, V81, P2137
[6]
CHAPLIN H, 1982, THROMB HAEMOSTASIS, V43, P218
[7]
CHINOWSKY MS, 1991, SO MED J, V83, P374
[8]
HEMOGLOBIN-S-C DISEASE IN A PREGNANT WOMAN WITH CRISIS AND FAT EMBOLIZATION SYNDROME [J].
CHMEL, H ;
BERTLES, JF .
AMERICAN JOURNAL OF MEDICINE, 1975, 58 (04) :563-566
[9]
CRYER PE, 1980, AM J MED, V68, P267
[10]
DECEULAER K, 1982, LANCET, V2, P229