PORPHOBILINOGEN DEAMINASE IS UNSTABLE IN THE ABSENCE OF ITS SUBSTRATE

[1] ADENOSINE-DEAMINASE MESSENGER-RNAS IN LYMPHOBLAST CELL-LINES DERIVED FROM LEUKEMIC PATIENTS AND PATIENTS WITH HEREDITARY ADENOSINE-DEAMINASE DEFICIENCY [J]. JOURNAL OF CLINICAL INVESTIGATION, 1983, 71 (06) : 1649 - 1660

[2] ANDERSON PM, 1980, J BIOL CHEM, V255, P1993

[3] CHARACTERIZATION OF THE PORPHOBILINOGEN DEAMINASE DEFICIENCY IN ACUTE INTERMITTENT PORPHYRIA - IMMUNOLOGICAL EVIDENCE FOR HETEROGENEITY OF THE GENETIC-DEFECT [J]. JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (01) : 1 - 12

[4] BATTERSBY A, 1983, J CHEM SOC PERK T, V1, P3031

[5] EFFECTS OF SUCCINYLACETONE ON DIMETHYLSULFOXIDE-MEDIATED INDUCTION OF HEME PATHWAY ENZYMES IN MOUSE FRIEND VIRUS-TRANSFORMED ERYTHROLEUKEMIA-CELLS [J]. EXPERIMENTAL CELL RESEARCH, 1984, 154 (02) : 474 - 484

[6] CHANG CS, 1984, BLOOD, V64, P64

[7] THE EFFECT OF N-METHYLPROTOPORPHYRIN AND SUCCINYL-ACETONE ON THE REGULATION OF HEME-BIOSYNTHESIS IN CHICKEN HEPATOCYTES IN CULTURE [J]. FEBS LETTERS, 1983, 159 (1-2) : 127 - 131

[8] ACUTE INTERMITTENT PORPHYRIA - CHARACTERIZATION OF A NOVEL MUTATION IN THE STRUCTURAL GENE FOR PORPHOBILINOGEN DEAMINASE - DEMONSTRATION OF NONCATALYTIC ENZYME INTERMEDIATES STABILIZED BY BOUND SUBSTRATE [J]. JOURNAL OF CLINICAL INVESTIGATION, 1985, 76 (02) : 865 - 874

[9] SUCCINYLACETONE, A POTENT INHIBITOR OF HEME-BIOSYNTHESIS - EFFECT ON CELL-GROWTH, HEME CONTENT AND DELTA-AMINOLEVULINIC-ACID DEHYDRATASE ACTIVITY OF MALIGNANT MURINE ERYTHROLEUKEMIA-CELLS [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1979, 88 (04) : 1382 - 1390

[10] GRANDCHAMP B, 1985, J BIOL CHEM, V260, P9630

[1] ADENOSINE-DEAMINASE MESSENGER-RNAS IN LYMPHOBLAST CELL-LINES DERIVED FROM LEUKEMIC PATIENTS AND PATIENTS WITH HEREDITARY ADENOSINE-DEAMINASE DEFICIENCY [J]. JOURNAL OF CLINICAL INVESTIGATION, 1983, 71 (06) : 1649 - 1660

[2] ANDERSON PM, 1980, J BIOL CHEM, V255, P1993

[3] CHARACTERIZATION OF THE PORPHOBILINOGEN DEAMINASE DEFICIENCY IN ACUTE INTERMITTENT PORPHYRIA - IMMUNOLOGICAL EVIDENCE FOR HETEROGENEITY OF THE GENETIC-DEFECT [J]. JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (01) : 1 - 12

[4] BATTERSBY A, 1983, J CHEM SOC PERK T, V1, P3031

[5] EFFECTS OF SUCCINYLACETONE ON DIMETHYLSULFOXIDE-MEDIATED INDUCTION OF HEME PATHWAY ENZYMES IN MOUSE FRIEND VIRUS-TRANSFORMED ERYTHROLEUKEMIA-CELLS [J]. EXPERIMENTAL CELL RESEARCH, 1984, 154 (02) : 474 - 484

[6] CHANG CS, 1984, BLOOD, V64, P64

[7] THE EFFECT OF N-METHYLPROTOPORPHYRIN AND SUCCINYL-ACETONE ON THE REGULATION OF HEME-BIOSYNTHESIS IN CHICKEN HEPATOCYTES IN CULTURE [J]. FEBS LETTERS, 1983, 159 (1-2) : 127 - 131

[8] ACUTE INTERMITTENT PORPHYRIA - CHARACTERIZATION OF A NOVEL MUTATION IN THE STRUCTURAL GENE FOR PORPHOBILINOGEN DEAMINASE - DEMONSTRATION OF NONCATALYTIC ENZYME INTERMEDIATES STABILIZED BY BOUND SUBSTRATE [J]. JOURNAL OF CLINICAL INVESTIGATION, 1985, 76 (02) : 865 - 874

[9] SUCCINYLACETONE, A POTENT INHIBITOR OF HEME-BIOSYNTHESIS - EFFECT ON CELL-GROWTH, HEME CONTENT AND DELTA-AMINOLEVULINIC-ACID DEHYDRATASE ACTIVITY OF MALIGNANT MURINE ERYTHROLEUKEMIA-CELLS [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1979, 88 (04) : 1382 - 1390

[10] GRANDCHAMP B, 1985, J BIOL CHEM, V260, P9630