GIANT SOMATOSENSORY EVOKED-POTENTIALS IN THE RETT SYNDROME

被引:30
作者
YOSHIKAWA, H
KAGA, M
SUZUKI, H
SAKURAGAWA, N
ARIMA, M
机构
[1] NATL CTR NEUROL & PSYCHIAT, NATL INST NEUROSCI, DIV INHERITED METAB DISORDERS, KODAIRA, TOKYO, JAPAN
[2] NATL INST MENTAL HLTH, ICHIKAWA, CHIBA, JAPAN
[3] NATL CTR NEUROL & PSYCHIAT, KOHNODAI HOSP, ICHIKAWA, CHIBA, JAPAN
关键词
RETT SYNDROME; SOMATOSENSORY EVOKED POTENTIALS; GIANT SOMATOSENSORY EVOKED POTENTIAL;
D O I
10.1016/S0387-7604(12)80295-6
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Somatosensory evoked potentials (SEP) were recorded in ten patients with the Rett syndrome. Seven cases showed abnormal SEP, and five of these cases showed giant SEP. The five cases with giant SEP were relatively young girls with epilepsy and parieto-central spikes on the electro-encephalogram (EEG). Older patients did not show giant SEP. These giant SEP may be the reflection of cortical hyperexcitability and they may subside as the disease progresses.
引用
收藏
页码:36 / 39
页数:4
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