PROLINE INCORPORATION BY CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH DUCHENNE MUSCULAR-DYSTROPHY

被引:10
作者
THOMPSON, RG
SPONDER, ES
ROSENMANN, E
HAMERTON, JL
WROGEMANN, K
机构
[1] UNIV MANITOBA,FAC MED,DEPT BIOCHEM,WINNIPEG R3E 0W3,MANITOBA,CANADA
[2] UNIV MANITOBA,FAC MED,DEPT PEDIAT GENET,WINNIPEG R3E 0W3,MANITOBA,CANADA
关键词
D O I
10.1016/0022-510X(82)90109-5
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:41 / 54
页数:14
相关论文
共 22 条
[1]   DECREASE IN THE RATE OF PROTEIN-SYNTHESIS BY POLYSOMES FROM CULTURED FIBROBLASTS OF PATIENTS AND CARRIERS WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
BOULE, M ;
VANASSE, M ;
BRAKIERGINGRAS, L .
CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES, 1979, 6 (03) :355-358
[2]   MICROTUBULE ORGANIZATION IN FIBROBLASTS FROM DYSTROPHIC CHICKENS AND PERSONS WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
CONNOLLY, JA ;
KALNINS, VI ;
BARBER, BH .
NATURE, 1979, 282 (5738) :511-513
[3]  
CULLEN MJ, 1977, LANCET, V2, P929
[4]  
DAVIS MH, 1980, J CELL BIOL, V87, pA203
[5]  
GELMAN, 1980, J CLIN INVEST, V65, P1398
[6]   STRUCTURAL-CHANGES IN LYSOSOMES FROM CULTURED HUMAN-FIBROBLASTS IN DUCHENNES MUSCULAR-DYSTROPHY [J].
GELMAN, BB ;
DAVIS, MH ;
MORRIS, RE ;
GRUENSTEIN, E .
JOURNAL OF CELL BIOLOGY, 1981, 88 (02) :329-337
[7]   FIBROBLAST-CULTURES IN DUCHENNE MUSCULAR-DYSTROPHY - ALTERATIONS IN SYNTHESIS AND SECRETION OF COLLAGEN AND NON-COLLAGEN PROTEINS [J].
IONASESCU, V ;
LARABRAUD, C ;
ZELLWEGER, H ;
IONASESCU, R ;
BURMEISTER, L .
ACTA NEUROLOGICA SCANDINAVICA, 1977, 55 (05) :407-417
[8]   REDUCED ADHESIVENESS BETWEEN SKIN FIBROBLASTS FROM PATIENTS WITH DUCHENNE MUSCULAR-DYSTROPHY [J].
JONES, GE ;
WITKOWSKI, JA .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1979, 43 (03) :465-470
[9]   PHOSPHOLIPID COMPOSITION OF CULTIVATED SKIN FIBROBLASTS IN DUCHENNES MUSCULAR-DYSTROPHY [J].
KOHLSCHUTTER, A ;
WIESMANN, UN ;
HERSCHKOWITZ, NN ;
FERBER, E .
CLINICA CHIMICA ACTA, 1976, 70 (03) :463-465
[10]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265