BIOCHEMICAL-EVIDENCE OF CARNITINE EFFECT ON PROPIONATE ELIMINATION

被引:9
作者
SUGIYAMA, N [1 ]
MORISHITA, H [1 ]
NAGAYA, S [1 ]
NAKAJIMA, T [1 ]
KAWASE, A [1 ]
OHYA, A [1 ]
SUGIYAMA, S [1 ]
KAMIYA, K [1 ]
WATANABE, I [1 ]
TOGARI, H [1 ]
KOBAYASHI, M [1 ]
OGAWA, Y [1 ]
WADA, Y [1 ]
机构
[1] NAGOYA CITY UNIV,SCH MED,DEPT PEDIAT,MIZUHO KU,NAGOYA,AICHI 467,JAPAN
关键词
D O I
10.1007/BF01801775
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:137 / 138
页数:2
相关论文
共 6 条
  • [1] PROPIONYLCARNITINE PHYSIOLOGICAL VARIATIONS IN VIVO
    BOHMER, T
    BREMER, J
    [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 152 (03) : 559 - &
  • [2] GOMPERTZ D, 1975, CLIN GENET, V8, P244
  • [3] ROE CR, 1982, LANCET, V1, P1411
  • [4] ROSENBERG LE, 1983, METABOLIC BASIS INHE, P474
  • [5] DIETARY THERAPY IN A GIRL WITH PROPIONIC ACIDEMIA - SUPPLEMENT WITH LEUCINE RESULTED IN CATCH UP GROWTH
    SATOH, T
    NARISAWA, K
    TAZAWA, Y
    SUZUKI, H
    HAYASAKA, K
    TADA, K
    KAWAKAMI, T
    [J]. TOHOKU JOURNAL OF EXPERIMENTAL MEDICINE, 1983, 139 (04) : 411 - 415
  • [6] DIFFERENT KETOGENIC RESPONSE TO MEDIUM-CHAIN TRIGLYCERIDES AND TO LONG-CHAIN TRIGLYCERIDES IN A CASE OF MUSCULAR CARNITINE PALMITOYLTRANSFERASE DEFICIENCY
    SUGIYAMA, N
    WADA, Y
    MORISHITA, H
    NONAKA, I
    [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1982, 5 (04) : 233 - 234