NUCLEOTIDE AND DEDUCED AMINO-ACID SEQUENCE OF THE E1-ALPHA SUBUNIT OF HUMAN-LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE

被引：38

作者：

ZHANG, B

CRABB, DW

HARRIS, RA

机构：

[1] INDIANA UNIV,SCH MED,DEPT BIOCHEM,635 BARNHILL DR,INDIANAPOLIS,IN 46223

[2] INDIANA UNIV,SCH MED,DEPT MED,INDIANAPOLIS,IN 46223

来源：

GENE | 1988年 / 69卷 / 01期

关键词：

D O I：

10.1016/0378-1119(88)90390-3

中图分类号：

Q3 [遗传学];

学科分类号：

071007 ; 090102 ;

摘要：

引用

页码：159 / 164

页数：6

共 22 条

[1] ISOLATION OF BIOLOGICALLY-ACTIVE RIBONUCLEIC-ACID FROM SOURCES ENRICHED IN RIBONUCLEASE [J].

CHIRGWIN, JM ;

PRZYBYLA, AE ;

MACDONALD, RJ ;

RUTTER, WJ .

BIOCHEMISTRY, 1979, 18 (24) :5294-5299

[2]

CHUANG DT, 1982, AM J HUM GENET, V34, P416

[3] AMINO-ACID-SEQUENCE AT THE MAJOR PHOSPHORYLATION SITE ON BOVINE KIDNEY BRANCHED-CHAIN 2-OXOACID DEHYDROGENASE COMPLEX [J].

COOK, KG ;

LAWSON, R ;

YEAMAN, SJ ;

AITKEN, A .

FEBS LETTERS, 1983, 164 (01) :47-50

[4]

DAHL HHM, 1987, J BIOL CHEM, V262, P7398

[5] PURIFICATION AND PROPERTIES OF BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE PHOSPHATASE FROM BOVINE KIDNEY [J].

DAMUNI, Z ;

MERRYFIELD, ML ;

HUMPHREYS, JS ;

REED, LJ .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (14) :4335-4338

[6] ABSENCE OF BRANCHED-CHAIN ACYL-TRANSFERASE AS A CAUSE OF MAPLE SYRUP URINE DISEASE [J].

DANNER, DJ ;

ARMSTRONG, N ;

HEFFELFINGER, SC ;

SEWELL, ET ;

PRIEST, JH ;

ELSAS, LJ .

JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (03) :858-860

[7]

DEMEIRLEIR L, 1988, J BIOL CHEM, V263, P1191

[8] INACTIVATION OF PURIFIED OX KIDNEY BRANCHED-CHAIN 2-OXOACID DEHYDROGENASE COMPLEX BY PHOSPHORYLATION [J].

FATANIA, H ;

LAU, KS ;

RANDLE, PJ .

FEBS LETTERS, 1981, 132 (02) :285-288

[9] PHYSIOLOGICAL COVALENT REGULATION OF RAT-LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE [J].

HARRIS, RA ;

POWELL, SM ;

PAXTON, R ;

GILLIM, SE ;

NAGAE, H .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1985, 243 (02) :542-555

[10] ALTERED KINETIC-PROPERTIES OF THE BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE COMPLEX DUE TO MUTATION OF THE BETA-SUBUNIT OF THE BRANCHED-CHAIN ALPHA-KETO ACID DECARBOXYLASE (E1) COMPONENT IN LYMPHOBLASTOID-CELLS DERIVED FROM PATIENTS WITH MAPLE SYRUP URINE DISEASE [J].

INDO, Y ;

KITANO, A ;

ENDO, F ;

AKABOSHI, I ;

MATSUDA, I .

JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (01) :63-70

← 1 2 3 →