STEROID-RESPONSIVE MYALGIA IN A PATIENT WITH BECKER MUSCULAR-DYSTROPHY

被引:7
作者
HIGUCHI, I [1 ]
NAKAMURA, K [1 ]
NAKAGAWA, M [1 ]
NAKAMURA, N [1 ]
USUKI, F [1 ]
INOSE, M [1 ]
OSAME, M [1 ]
机构
[1] NCNP,NATL INST NEUROSCI,KODAIRA,TOKYO,JAPAN
关键词
BECKER MUSCULAR DYSTROPHY; MYALGIA; STEROID THERAPY; MENTAL RETARDATION; CARDIOMYOPATHY;
D O I
10.1016/0022-510X(93)90228-Q
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a male patient with exercise-induced focal myalgia in the leg muscles. Dystrophin immunostaining of a biopsied muscle specimen from the patient showed the absence of or only faint immunoreactivity in 20% of the muscle fibers. The patient was diagnosed as having Becker muscular dystrophy. The myalgia was intractable and did not respond to non-steroidal anti-inflammatory drugs. The patient was placed on prednisone and found to be sensitive to it. Although he had recurrences of the symptom during tapering of the steroid, slower tapering over one year was tolerated. Steroid treatment may be useful for other Becker muscular dystrophy patients with myalgia.
引用
收藏
页码:219 / 222
页数:4
相关论文
共 29 条
[1]  
ABE M, 1990, BRAIN NEXRVE, V42, P1061
[2]   MYOCARDIAL PATCHY STAINING OF DYSTROPHIN IN BECKERS MUSCULAR-DYSTROPHY ASSOCIATED WITH CARDIOMYOPATHY [J].
ANAN, R ;
HIGUCHI, I ;
ICHINARI, K ;
KUBOTA, K ;
KISANUKI, A ;
ARIMA, S ;
NAKAO, S ;
OSAME, M ;
TANAKA, H .
AMERICAN HEART JOURNAL, 1992, 123 (04) :1088-1089
[3]   DYSTROPHIN DIAGNOSIS - COMPARISON OF DYSTROPHIN ABNORMALITIES BY IMMUNOFLUORESCENCE AND IMMUNOBLOT ANALYSES [J].
ARAHATA, K ;
HOFFMAN, EP ;
KUNKEL, LM ;
ISHIURA, S ;
TSUKAHARA, T ;
ISHIHARA, T ;
SUNOHARA, N ;
NONAKA, I ;
OZAWA, E ;
SUGITA, H .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1989, 86 (18) :7154-7158
[4]  
BEGGS AH, 1990, HUM GENET, V86, P45
[5]   DYSTROPHIN EXPRESSION AND SOMATIC REVERSION IN PREDNISONE-TREATED AND UNTREATED DUCHENNE DYSTROPHY [J].
BURROW, KL ;
COOVERT, DD ;
KLEIN, CJ ;
BULMAN, DE ;
KISSEL, JT ;
RAMMOHAN, KW ;
BURGHES, AHM ;
MENDELL, JR .
NEUROLOGY, 1991, 41 (05) :661-666
[6]   DELETION SCREENING OF THE DUCHENNE MUSCULAR-DYSTROPHY LOCUS VIA MULTIPLEX DNA AMPLIFICATION [J].
CHAMBERLAIN, JS ;
GIBBS, RA ;
RANIER, JE ;
NGUYEN, PN ;
CASKEY, CT .
NUCLEIC ACIDS RESEARCH, 1988, 16 (23) :11141-11156
[7]   VERY MILD MUSCULAR-DYSTROPHY ASSOCIATED WITH THE DELETION OF 46-PERCENT OF DYSTROPHIN [J].
ENGLAND, SB ;
NICHOLSON, LVB ;
JOHNSON, MA ;
FORREST, SM ;
LOVE, DR ;
ZUBRZYCKAGAARN, EE ;
BULMAN, DE ;
HARRIS, JB ;
DAVIES, KE .
NATURE, 1990, 343 (6254) :180-182
[8]   LONG-TERM BENEFIT FROM PREDNISONE THERAPY IN DUCHENNE MUSCULAR-DYSTROPHY [J].
FENICHEL, GM ;
FLORENCE, JM ;
PESTRONK, A ;
MENDELL, JR ;
MOXLEY, RT ;
GRIGGS, RC ;
BROOKE, MH ;
MILLER, JP ;
ROBISON, J ;
KING, W ;
SIGNORE, L ;
PANDYA, S ;
SCHIERBECKER, J ;
WILSON, B .
NEUROLOGY, 1991, 41 (12) :1874-1877
[9]   FAMILIAL X-LINKED MYALGIA AND CRAMPS - A NONPROGRESSIVE MYOPATHY ASSOCIATED WITH A DELETION IN THE DYSTROPHIN GENE [J].
GOSPE, SM ;
LAZARO, RP ;
LAVA, NS ;
GROOTSCHOLTEN, PM ;
SCOTT, MO ;
FISCHBECK, KH .
NEUROLOGY, 1989, 39 (10) :1277-1280
[10]  
HATAE T, 1991, CLIN NEUROL, V31, P1155