DEFECTIVE CA2+-INDUCED MICROVESICULATION AND DEFICIENT EXPRESSION OF PROCOAGULANT ACTIVITY IN ERYTHROCYTES FROM A PATIENT WITH A BLEEDING DISORDER - A STUDY OF THE RED-BLOOD-CELLS OF SCOTT SYNDROME

被引:130
作者
BEVERS, EM
WIEDMER, T
COMFURIUS, P
SHATTIL, SJ
WEISS, HJ
ZWAAL, RFA
SIMS, PJ
机构
[1] OKLAHOMA MED RES FDN,CARDIOVASC BIOL RES PROGRAM,825 NE 13TH ST,OKLAHOMA CITY,OK 73104
[2] UNIV LIMBURG,CARDIOVASC RES INST,DEPT BIOCHEM,6200 MD MAASTRICHT,NETHERLANDS
[3] UNIV PENN,SCH MED,HEMATOL ONCOL SECT,PHILADELPHIA,PA 19104
[4] UNIV OKLAHOMA,HLTH SCI CTR,DEPT MED,OKLAHOMA CITY,OK 73190
[5] UNIV PENN,SCH MED,DEPT MED,PHILADELPHIA,PA 19104
[6] UNIV OKLAHOMA,HLTH SCI CTR,DEPT PATHOL,OKLAHOMA CITY,OK 73190
[7] UNIV PENN,SCH MED,DEPT PATHOL & LAB MED,PHILADELPHIA,PA 19104
[8] UNIV OKLAHOMA,HLTH SCI CTR,DEPT MICROBIOL & IMMUNOL,OKLAHOMA CITY,OK 73190
[9] ST LUKES ROOSEVELT HOSP,DIV HEMATOL ONCOL,NEW YORK,NY 10025
[10] COLUMBIA UNIV COLL PHYS & SURG,DEPT MED,NEW YORK,NY 10032
关键词
D O I
10.1182/blood.V79.2.380.380
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:380 / 388
页数:9
相关论文
共 23 条
[1]   PLATELET RECEPTOR MEDIATED FACTOR-X ACTIVATION BY FACTOR-IXA - HIGH-AFFINITY FACTOR-IXA RECEPTORS INDUCED BY FACTOR-VIII ARE DEFICIENT ON PLATELETS IN SCOTT SYNDROME [J].
AHMAD, SS ;
RAWALASHEIKH, R ;
ASHBY, B ;
WALSH, PN .
JOURNAL OF CLINICAL INVESTIGATION, 1989, 84 (03) :824-828
[2]   CA-2+-INDUCED BIOCHEMICAL-CHANGES IN HUMAN-ERYTHROCYTES AND THEIR RELATION TO MICROVESICULATION [J].
ALLAN, D ;
THOMAS, P .
BIOCHEMICAL JOURNAL, 1981, 198 (03) :433-440
[3]   CALCIUM ION-DEPENDENT DIACYLGLYCEROL ACCUMULATION IN ERYTHROCYTES IS ASSOCIATED WITH MICRO-VESICULATION BUT NOT WITH EFFLUX OF POTASSIUM-IONS [J].
ALLAN, D ;
MICHELL, RH .
BIOCHEMICAL JOURNAL, 1977, 166 (03) :495-499
[4]   LOSS OF MEMBRANE PHOSPHOLIPID ASYMMETRY IN PLATELETS AND RED-CELLS MAY BE ASSOCIATED WITH CALCIUM-INDUCED SHEDDING OF PLASMA-MEMBRANE AND INHIBITION OF AMINOPHOSPHOLIPID TRANSLOCASE [J].
COMFURIUS, P ;
SENDEN, JMG ;
TILLY, RHJ ;
SCHROIT, AJ ;
BEVERS, EM ;
ZWAAL, RFA .
BIOCHIMICA ET BIOPHYSICA ACTA, 1990, 1026 (02) :153-160
[5]   MAINTENANCE OF LIPID ASYMMETRY IN RED-BLOOD-CELLS AND GHOSTS - EFFECT OF DIVALENT-CATIONS AND SERUM-ALBUMIN ON THE TRANSBILAYER DISTRIBUTION OF PHOSPHATIDYLSERINE [J].
CONNOR, J ;
GILLUM, K ;
SCHROIT, AJ .
BIOCHIMICA ET BIOPHYSICA ACTA, 1990, 1025 (01) :82-86
[6]   AMINOPHOSPHOLIPID TRANSLOCATION IN ERYTHROCYTES - EVIDENCE FOR THE INVOLVEMENT OF A SPECIFIC TRANSPORTER AND AN ENDOFACIAL PROTEIN [J].
CONNOR, J ;
SCHROIT, AJ .
BIOCHEMISTRY, 1990, 29 (01) :37-43
[7]   LIPID POLYMORPHISM AND THE FUNCTIONAL ROLES OF LIPIDS IN BIOLOGICAL-MEMBRANES [J].
CULLIS, PR ;
DEKRUIJFF, B .
BIOCHIMICA ET BIOPHYSICA ACTA, 1979, 559 (04) :399-420
[8]   STATIC AND DYNAMIC LIPID ASYMMETRY IN CELL-MEMBRANES [J].
DEVAUX, PF .
BIOCHEMISTRY, 1991, 30 (05) :1163-1173
[9]  
FOX JEB, 1990, BLOOD, V76, P2510
[10]  
FOX JEB, 1983, J BIOL CHEM, V258, P9973