INCONTINENTIA-PIGMENTI (BLOCH-SULZBERGER SYNDROME) MANIFESTING AS PAINFUL PERIUNGUAL AND SUBUNGUAL TUMORS

被引：15

作者：

ADENIRAN, A ^{[1
]}

TOWNSEND, PLG ^{[1
]}

PEACHEY, RDG ^{[1
]}

机构：

[1] FRENCHAY HOSP,DEPT PLAST SURG,BRISTOL BS16 1LE,AVON,ENGLAND

来源：

JOURNAL OF HAND SURGERY-BRITISH AND EUROPEAN VOLUME | 1993年 / 18B卷 / 05期

关键词：

D O I：

10.1016/0266-7681(93)90031-A

中图分类号：

R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学（修复外科学）];

学科分类号：

摘要：

A 25-year-old lady presented with painful periungual tumours which were associated with lytic changes of underlying terminal phalanges. She had been previously treated as a case of chronic paronychia but the problem recurred. She was subsequently diagnosed as a case of Incontinentia pigmenti which is a rare genodermatosis with mixed ectodermal and mesodermal polydysplasias, onchychodystrophy being a very rare manifestation. She was treated by excision of painful finger lesions, but there is no specific treatment for the underlying condition.

引用

页码：667 / 669

页数：3

共 10 条

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