IMBALANCE OF LIVER PHOSPHORYLASE AND ACCUMULATION OF HEPATIC GLYCOGEN IN A GIRL WITH PROGRESSIVE DISEASE OF BRAIN

被引:25
作者
HUG, G
SCHUBERT, WK
SCHWACHM.H
机构
关键词
D O I
10.1016/S0022-3476(65)80362-6
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:741 / +
页数:1
相关论文
共 11 条
[1]  
CORI CF, 1947, POLYSACCHARIDE PHOSP, P216
[2]   EFFECTS OF MONOAMINE OXIDASE INHIBITION ON BIOGENIC AMINE METABOLISM [J].
GOLDSTEIN, M ;
MUSACCHIO, JM .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1963, 107 (03) :840-+
[3]  
HERS H G, 1959, Rev Int Hepatol, V9, P35
[4]   MENGHINI NEEDLE BIOPSY OF THE LIVER [J].
HONG, R ;
SCHUBERT, WK .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1960, 100 (01) :42-46
[5]   CORIS DISEASE (AMYLO-1.6-GLUCOSIDASE DEFICIENCY) - REPORT OF A CASE IN A NEGRO CHILD [J].
HUG, G ;
GUEST, GM ;
KRILL, CE ;
PERRIN, EV .
NEW ENGLAND JOURNAL OF MEDICINE, 1963, 268 (03) :115-&
[6]   GLYCOGEN STORAGE DISEASE [J].
ILLINGWORTH, B .
AMERICAN JOURNAL OF CLINICAL NUTRITION, 1961, 9 (06) :683-&
[7]   CHRONIC PROGRESSIVE MYOPATHY WITH MYOGLOBINURIA - DEMONSTRATION OF A GLYCOGENOLYTIC DEFECT IN THE MUSCLE [J].
SCHMID, R ;
MAHLER, R .
JOURNAL OF CLINICAL INVESTIGATION, 1959, 38 (11) :2044-2058
[8]  
SUTHERLAND EW, 1962, J BIOL CHEM, V237, P1220
[9]   POLYSACCHARIDE PHOSPHORYLASE, LIVER [J].
SUTHERLAND, EW .
METHODS IN ENZYMOLOGY, 1955, 1 :215-222
[10]  
SUTHERLAND EW, 1961, HARVEY LECT, V57, P17