PERSISTENT MULLERIAN DUCT SYNDROME - REPORT OF 2 BOYS WITH ASSOCIATED CROSSED TESTICULAR ECTOPIA

被引:11
作者
MAHFOUZ, EH
ISSA, MA
FARAG, TI
NAGUIB, KK
ALAWADI, SA
SCHIMKE, RN
机构
[1] KANSAS UNIV,SCH MED,KANSAS CITY,KS 66103
[2] IBN SINA HOSP,DEPT PAEDIAT SURG,KUWAIT,KUWAIT
[3] KUWAIT MED GENET CTR,KUWAIT,KUWAIT
关键词
Crossed testicular ectopia;
D O I
10.1016/0022-3468(90)90367-I
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Persistent Mullerian duct structures and crossed testicular ectopia were found in two phenotypically normal, unrelated males, with 46,XY karyotype, during routine herniorrhaphy. In each case, the vascular supply to the ectopic testis originated from the appropriate ipsilateral side. The clinical significance and genetic implications of this rare association are discussed. © 1990.
引用
收藏
页码:692 / 693
页数:2
相关论文
共 11 条
[1]   FAMILIAL PERSISTENT MULLERIAN DUCT SYNDROME [J].
BEHESHTI, M ;
CHURCHILL, BM ;
HARDY, BE ;
BAILEY, JD ;
WEKSBERG, R ;
ROGAN, GF .
JOURNAL OF UROLOGY, 1984, 131 (05) :968-969
[2]   ISOLATION OF THE BOVINE AND HUMAN GENES FOR MULLERIAN INHIBITING SUBSTANCE AND EXPRESSION OF THE HUMAN-GENE IN ANIMAL-CELLS [J].
CATE, RL ;
MATTALIANO, RJ ;
HESSION, C ;
TIZARD, R ;
FARBER, NM ;
CHEUNG, A ;
NINFA, EG ;
FREY, AZ ;
GASH, DJ ;
CHOW, EP ;
FISHER, RA ;
BERTONIS, JM ;
TORRES, G ;
WALLNER, BP ;
RAMACHANDRAN, KL ;
RAGIN, RC ;
MANGANARO, TF ;
MACLAUGHLIN, DT ;
DONAHOE, PK .
CELL, 1986, 45 (05) :685-698
[3]   MAPPING OF THE GENE FOR ANTI-MULLERIAN HORMONE TO THE SHORT ARM OF HUMAN CHROMOSOME-19 [J].
COHENHAGUENAUER, O ;
PICARD, JY ;
MATTEI, MG ;
SERERO, S ;
NGUYEN, VC ;
DETAND, MF ;
GUERRIER, D ;
HORSCAYLA, MC ;
JOSSO, N ;
FREZAL, J .
CYTOGENETICS AND CELL GENETICS, 1987, 44 (01) :2-6
[4]   TRANSVERSE TESTICULAR ECTOPIA WITH PERSISTENT MULLERIAN DUCT [J].
FOURCROY, JL ;
BELMAN, AB .
UROLOGY, 1982, 19 (05) :536-538
[5]   PERSISTENT MULLERIAN STRUCTURES IN INFERTILE MALE [J].
HERSHLAG, A ;
SPITZ, IM ;
HOCHNERCELNIKIER, D ;
HASKEL, Y ;
LERNAU, DZ ;
NISSAN, S ;
ROSENMANN, A ;
ROSENMANN, E .
UROLOGY, 1986, 28 (02) :138-141
[6]   INTRA-ABDOMINAL SEMINOMAS IN PERSISTENT MULLERIAN DUCT SYNDROME [J].
KAZIM, E .
UROLOGY, 1985, 26 (03) :290-292
[7]   THE INFLUENCE OF NEONATAL ORCHIOPEXY UPON THE TESTIS IN PERSISTENT MULLERIAN DUCT SYNDROME [J].
MELMAN, A ;
LEITER, E ;
PEREZ, JM ;
DRISCOLL, D ;
PALMER, C .
JOURNAL OF UROLOGY, 1981, 125 (06) :856-858
[8]  
Nilson O, 1939, ACTA CHIR SCAND, V83, P231
[9]   PERSISTENT MULLERIAN DUCT SYNDROME - REVIEW AND REPORT OF 3 CASES [J].
SHEEHAN, SJ ;
TOBBIA, IN ;
ISMAIL, MA ;
KELLY, DG ;
DUFF, FA .
BRITISH JOURNAL OF UROLOGY, 1985, 57 (05) :548-551
[10]  
SIMPSON JL, 1976, DISORDERS SEXUAL DIF, P194