MOLECULAR-BASIS OF LYSOSOMAL ACCUMULATION OF SUBUNIT-C OF MITOCHONDRIAL ATP SYNTHASE IN NEURONAL CEROID-LIPOFUSCINOSIS

被引：9

作者：

EZAKI, J ^{[1
]}

WOLFE, LS ^{[1
]}

KOMINAMI, E ^{[1
]}

机构：

[1] MCGILL UNIV,MONTREAL NEUROL INST & HOSP,MONTREAL H3A 2B4,QUEBEC,CANADA

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1993年 / 16卷 / 02期

关键词：

D O I：

10.1007/BF00710269

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

[No abstract available]

引用

页码：296 / 298

页数：3

共 7 条

[1] THE SEQUENCE OF THE MAJOR PROTEIN STORED IN OVINE CEROID LIPOFUSCINOSIS IS IDENTICAL WITH THAT OF THE DICYCLOHEXYLCARBODIIMIDE-REACTIVE PROTEOLIPID OF MITOCHONDRIAL ATP SYNTHASE [J].

FEARNLEY, IM ;

WALKER, JE ;

MARTINUS, RD ;

JOLLY, RD ;

KIRKLAND, KB ;

SHAW, GJ ;

PALMER, DN .

BIOCHEMICAL JOURNAL, 1990, 268 (03) :751-758

[2] LYSOSOMAL STORAGE OF SUBUNIT-C OF MITOCHONDRIAL ATP SYNTHASE IN BATTEN DISEASE (CEROID-LIPOFUSCINOSIS) [J].

HALL, NA ;

LAKE, BD ;

DEWJI, NN ;

PATRICK, AD .

BIOCHEMICAL JOURNAL, 1991, 275 :269-272

[3] INFANTILE FORM OF NEURONAL CEROID LIPOFUSCINOSIS (CLN1) MAPS TO THE SHORT ARM OF CHROMOSOME-1 [J].

JARVELA, I ;

SCHLEUTKER, J ;

HAATAJA, L ;

SANTAVUORI, P ;

PUHAKKA, L ;

MANNINEN, T ;

PALOTIE, A ;

SANDKUIJL, LA ;

RENLUND, M ;

WHITE, R ;

AULA, P ;

PELTONEN, L .

GENOMICS, 1991, 9 (01) :170-173

[4]

KOMINAMI E, 1983, J BIOL CHEM, V258, P6093

[5] SPECIFIC STORAGE OF SUBUNIT C OF MITOCHONDRIAL ATP SYNTHASE IN LYSOSOMES OF NEURONAL CEROID LIPOFUSCINOSIS (BATTENS DISEASE) [J].

KOMINAMI, E ;

EZAKI, J ;

MUNO, D ;

ISHIDO, K ;

UENO, T ;

WOLFE, LS .

JOURNAL OF BIOCHEMISTRY, 1992, 111 (02) :278-282

[6]

PALMER DN, 1989, J BIOL CHEM, V264, P5736

[7]

PALMER DN, 1990, ADV EXP MED BIOL, V266, P211

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