ELECTROPHORETIC FORMS OF HUMAN LIVER ALPHA-L-FUCOSIDASE AND THEIR RELATIONSHIP TO FUCOSIDOSIS (MUCOPOLYSACCHARIDOSIS F)

被引:58
作者
ALHADEFF, JA
MILLER, AL
WENGER, DA
OBRIEN, JS
机构
[1] UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
[2] UNIV COLORADO,MED CTR,DEPT PEDIAT,DENVER,CO 80220
关键词
D O I
10.1016/0009-8981(74)90412-4
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:307 / 313
页数:7
相关论文
共 14 条
  • [1] FUCOSIDOSIS
    DURAND, P
    BORRONE, C
    DELLACEL.G
    [J]. JOURNAL OF PEDIATRICS, 1969, 75 (04) : 665 - &
  • [2] GATTI R, 1973, LANCET, V2, P1024
  • [3] HAGLUND H, 1967, SCIENCE TOOLS, V14, P1
  • [4] KOUSSEFF BG, 1973, LANCET, V2, P1387
  • [5] The determination of enzyme dissociation constants
    Lineweaver, H
    Burk, D
    [J]. JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1934, 56 : 658 - 666
  • [6] LOEB H, 1969, HELV PAEDIATR ACTA, V24, P519
  • [7] HUMAN LIVER ALPHA-L-FUCOSIDASES
    ROBINSON, D
    THORPE, R
    [J]. CLINICA CHIMICA ACTA, 1973, 47 (03) : 403 - 407
  • [9] VANHOOF F, 1964, CR HEBD ACAD SCI, V259, P1281
  • [10] VANHOOF F, 1968, LANCET, V1, P1198