SURGICAL-TREATMENT OF SCOLIOSIS IN A SPINAL MUSCULAR-ATROPHY POPULATION

被引:42
作者
PHILLIPS, DP
ROYE, DP
FARCY, JPC
LEET, A
SHELTON, YA
机构
[1] Columbia-Presbyterian Medical Center, New York, NY
[2] Columbia University College of Physicians and Surgeons, New York, NY
[3] Alfred I. duPont Institute, Wilmington, DE
关键词
Paralytic scoliosis; Spinal muscular atrophy;
D O I
10.1097/00007632-199009000-00019
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Seventy-eight patients were diagnosed with spinal mus-cular atrophy between 1969 and 1988. Scoliosis developed in 34 of these patients, an incidence of 60%. Thirty- one patients could be retrospectively reviewed by chart review or interview. The average follow-up was 11.5 years. Onset of scoliosis averaged 8.8 years. Twenty-two patients were treated nonsurgically and nine surgically. Patients had improved sitting balance and endurance after surgery. Complications of surgery included loss of correction in one patient, one pseudarthrosis, and one patient who required prolonged ventilatory support. The prolonged survival of patients with spinal muscular atrophy justifies aggressive orthopaedic management of scoliosis to prevent progression of deformity and improve sitting comfort. © Lippincott-Raven Publishers.
引用
收藏
页码:942 / 945
页数:4
相关论文
共 13 条
[1]  
Aprin H., Bowen J.R., Macewen G.D., Hall J.E., Spine fusion in patients with spinal muscular atrophy, J Bone Joint Surg, 64A, pp. 1179-1187, (1982)
[2]  
Benady S.G., Spinal muscular atrophy in childhood: Review of 50 cases, Develop Med Child Neurol, 20, pp. 746-757, (1978)
[3]  
Brown J.C., Zeller J.L., Swank S.M., Furumasu J., Warath S.L., Surgical and functional results of spine fusion in spinal muscular atrophy, Spine, 14, pp. 763-770, (1989)
[4]  
Byers R.K., Banker B.Q., Infantile muscular atrophy, Arch Neurol, (1961)
[5]  
Daher Y.H., Lonstein J.E., Winter R.B., Bradford D.S., Spinal surgery in spinal muscular atrophy, J Pediatr Orthop, 5, pp. 391-395, (1985)
[6]  
Dubousset J., Herring J.A., Shufflebarger H., The crankshaft phenomenon, J Pediatr Orthop, 9, pp. 541-550, (1989)
[7]  
Dubowitz V., Infantile muscular atrophy. A prospective study with particular reference to a slowly progressive variety, Brain, 87, pp. 707-717, (1964)
[8]  
Evans G.A., Drennan J.C., Russman B.S., Functional classification and orthopaedic management of spinal muscular atrophy, J Bone Joint Surg, 63B, pp. 516-522, (1981)
[9]  
Furumasu J., Swank S.M., Brown J.C., Gilgoff I., Warath S., Zeller J., Functional activities in spinal muscular atrophy patients after spinal fusion, Spine, 14, pp. 771-775, (1989)
[10]  
Hensinger R.N., Macewen G.D., Spinal deformity associated with heritable neurological conditions: Spinal muscular atrophy, Friedreich’s ataxia, familial dysautonomia, and Charcot-Marie-Tooth disease, J Bone Joint Surg, 58A, pp. 13-23, (1976)