VARIABILITY IN PURIFIED DYSFUNCTIONAL C1-INHIBITOR PROTEINS FROM PATIENTS WITH HEREDITARY ANGIONEUROTIC-EDEMA - FUNCTIONAL AND ANALYTICAL GEL STUDIES

被引：55

作者：

DONALDSON, VH

HARRISON, RA

ROSEN, FS

BING, DH

KINDNESS, G

CANAR, J

WAGNER, CJ

AWAD, S

机构：

[1] UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

[2] UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT MED,CINCINNATI,OH 45229

[3] MRC CTR,MECH TUMOUR IMMUN UNIT,CAMBRIDGE CB2 2QH,ENGLAND

[4] HARVARD UNIV,SCH MED,DEPT PEDIAT,BOSTON,MA 02115

[5] BETH ISRAEL HOSP,BOSTON,MA 02215

[6] COLL TECHNOL DUNDEE,DEPT MOLEC,DUNDEE,SCOTLAND

[7] COLL TECHNOL DUNDEE,DEPT LIFE SCI,DUNDEE,SCOTLAND

来源：

关键词：

D O I：

10.1172/JCI111664

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：124 / 132

页数：9

共 33 条

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EVANS, RR
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