ADENOSINE-DEAMINASE AND IMMUNE DYSFUNCTION - BIOCHEMICAL CORRELATES DEFINED BY MOLECULAR ANALYSIS THROUGHOUT A DISEASE COURSE

被引:3
作者
COLEMAN, MS
DANTON, MJ
PHILIPS, A
机构
关键词
D O I
10.1111/j.1749-6632.1985.tb27096.x
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
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页码:54 / 65
页数:12
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共 22 条
[1]   IS TERMINAL DEOXYNUCLEOTIDYL TRANSFERASE A SOMATIC MUTAGEN IN LYMPHOCYTES [J].
BALTIMORE, D .
NATURE, 1974, 248 (5447) :409-411
[2]  
BOLLUM FJ, 1975, KA FORSTER LECTURES, V14, P1
[3]   LYMPHO-SPECIFIC TOXICITY IN ADENOSINE-DEAMINASE DEFICIENCY AND PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY - POSSIBLE ROLE OF NUCLEOSIDE KINASE(S) [J].
CARSON, DA ;
KAYE, J ;
SEEGMILLER, JE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (12) :5677-5681
[4]   DEOXYADENOSINE TRIPHOSPHATE AS A POTENTIALLY TOXIC METABOLITE IN ADENOSINE-DEAMINASE DEFICIENCY [J].
COHEN, A ;
HIRSCHHORN, R ;
HOROWITZ, SD ;
RUBINSTEIN, A ;
POLMAR, SH ;
HONG, R ;
MARTIN, DW .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1978, 75 (01) :472-476
[5]  
COLEMAN MS, 1978, J BIOL CHEM, V253, P1619
[6]   OVERPRODUCTION OF ADENINE DEOXYNUCLEOSIDES AND DEOXYNUCLEOTIDES IN ADENOSINE-DEAMINASE DEFICIENCY WITH SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].
DONOFRIO, J ;
COLEMAN, MS ;
HUTTON, JJ ;
DAOUD, A ;
LAMPKIN, B ;
DYMINSKI, J .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (04) :884-887
[7]   IMMUNOLOGICAL AND BIOCHEMICAL PROFILES IN RESPONSE TO TRANSFUSION THERAPY IN AN ADENOSINE DEAMINASE-DEFICIENT PATIENT WITH SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].
DYMINSKI, JW ;
DAOUD, A ;
LAMPKIN, BC ;
LIMOUZE, S ;
DONOFRIO, J ;
COLEMAN, MS ;
HUTTON, JJ .
CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1979, 14 (03) :307-326
[8]  
GIBLETT ER, 1972, LANCET, V2, P1067
[9]  
GREVER MR, 1981, BLOOD, V57, P406
[10]  
GREVER MR, 1984, CANCER TREAT S, V2, P43