PROGRESSIVE INTRAHEPATIC CHOLESTASIS (BYLERS DISEASE) - CASE-REPORT

被引:35
作者
VOS, RD
WOLFPEETERS, CD
DESMET, V
EGGERMONT, E
VANACKER, K
机构
[1] UNIV INSTELLING ANTWERPEN, KINDER GENEESKUNDE, ANTWERPEN, BELGIUM
[2] ACAD ZIEKENHUIS SINT RAFAEL, DEPT MED NAVORSING, LAB HISTOCHEM CYTOCHEM, MINDERBROEDERS STR 12, B-3000 LEUVEN, BELGIUM
[3] ACAD ZIEKENHUIS SINT RAFAEL, DEPT ONTWIKKELINGS BIOL, AFDELING PEDIAT, LEUVEN, BELGIUM
关键词
D O I
10.1136/gut.16.12.943
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:943 / 950
页数:8
相关论文
共 28 条
[1]  
BANFIELD WJ, 1974, GASTROENTEROLOGY, V67, P779
[2]  
CARR I, 1972, J ANAT, V112, P383
[3]   BYLER DISEASE - FATAL FAMILIAL INTRAHEPATIC CHOLESTASIS IN AN AMISH KINDRED [J].
CLAYTON, RJ ;
IBER, FL ;
RUEBNER, BH ;
MCKUSICK, VA .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1969, 117 (01) :112-&
[4]   BYLERS DISEASE - FATAL FAMILIAL INTRAHEPATIC CHOLESTASIS IN AN AMISH KINDRED [J].
CLAYTON, RJ ;
IBER, FL ;
RUEBNER, BH ;
MCKUSICK, VA .
JOURNAL OF PEDIATRICS, 1965, 67 (5P2) :1025-+
[5]  
Desmet V J, 1972, Prog Liver Dis, V4, P97
[6]   A NEW DIAZO REAGENT FOR SPECIFIC STAINING OF CONJUGATED BILIRUBIN IN TISSUE SECTIONS [J].
DESMET, VJ ;
BULLENS, AM ;
DEGROOTE, J ;
HEIRWEGH, KP .
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY, 1968, 16 (06) :419-&
[7]   SIGNIFICANCE OF LIVER CANALICULAR CHANGES AFTER EXPERIMENTAL BILE-DUCT LIGATION [J].
DEVOS, R ;
DEWOLFPEETERS, C ;
DESMET, V ;
BIANCHI, L ;
ROHR, HP .
EXPERIMENTAL AND MOLECULAR PATHOLOGY, 1975, 23 (01) :12-34
[8]   ELECTRON-MICROSCOPY AND MORPHOMETRY OF CANALICULAR DIFFERENTIATION IN FETAL AND NEONATAL RAT-LIVER [J].
DEWOLFPEETERS, C ;
DEVOS, R ;
DESMET, V ;
BIANCHI, L ;
ROHR, HP .
EXPERIMENTAL AND MOLECULAR PATHOLOGY, 1974, 21 (03) :339-350
[9]  
ENZAN H, 1974, ACTA PATHOL JAPON, V24, P427
[10]   BILIRUBIN CONJUGATES IN BILE OF MAN AND RAT IN NORMAL STATE AND IN LIVER-DISEASE [J].
FEVERY, J ;
VANDAMME, B ;
DEGROOTE, J ;
HEIRWEGH, KP ;
MICHIELS, R .
JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (09) :2482-+