CERVICAL NEUROSCHISIS AND MENINGOCELE MANQUE IN TYPE-I (NO NECK) KLIPPEL-FEIL SYNDROME

被引:11
作者
COCHRANE, DD
HASLAM, RHA
MYLES, ST
机构
[1] UNIV BRITISH COLUMBIA,DEPT SURG,VANCOUVER V6T 1W5,BC,CANADA
[2] UNIV TORONTO,DEPT PEDIAT,TORONTO M5S 1A1,ONTARIO,CANADA
[3] UNIV CALGARY,DEPT CLIN NEUROSCI,CALGARY T2N 1N4,ALBERTA,CANADA
关键词
KLIPPEL-FEIL SYNDROME; MENINGOCELE MANQUE; SPINAL CORD; DYSRAPHISM; NEUROSCHISIS;
D O I
10.1159/000120520
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A mate child with type I (no neck) Klippel-Feil syndrome presented at birth with a transient and partial cord injury. Investigations failed to reveal spinal instability or foramen magnum compression. Subsequent deterioration led to investigations that demonstrated neuroschisis. A cervical meningocoele manque with cord tethering was found at exploration and untethering reversed the deficit. The surgical pathology of the cervical cord is described.
引用
收藏
页码:174 / 178
页数:5
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