SYSTEMIC CAPILLARY LEAK SYNDROME

被引:27
作者
BARNADAS, MA
CISTERO, A
SITJAS, D
PASCUAL, E
PUIG, X
DEMORAGAS, JM
机构
[1] HOSP SANTA CRUZ & SAN PABLO,DEPT DERMATOL,E-08025 BARCELONA,SPAIN
[2] HOSP SANTA CRUZ & SAN PABLO,DEPT ALLERGY,E-08025 BARCELONA,SPAIN
[3] CENT HOSP MANRESA,DEPT INTERNAL MED,MANRESA,SPAIN
关键词
D O I
10.1016/0190-9622(95)90405-0
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Systemic capillary leak syndrome is a rare, severe disorder with a high mortality rate. It consists of the shift of fluid and proteins from the intravascular to the extravascular compartment with subsequent hypovolemic shock. We describe a 34-year-old-woman who had several episodes of generalized edema that evolved to hypovolemic shock. During the acute phase, laboratory investigations revealed marked hypoproteinemia, leukocytosis, and high levels of hematocrit and hemoglobin. A paraprotein IgG k chain was detected. Although different therapeutic trials were used, the patient continued to have similar episodes and she died during an acute episode 21/2 years after the first symptom of this disorder. The cause of systemic capillary leak syndrome is unknown. The presence of a paraprotein IgG is frequent in this group of patients.
引用
收藏
页码:364 / 366
页数:3
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