LINEAR GROWTH IN PATIENTS WITH TURNER SYNDROME - INFLUENCE OF SPONTANEOUS PUBERTY AND PARENTAL HEIGHT

被引:83
作者
MASSA, G [1 ]
VANDERSCHUERENLODEWEYCKX, M [1 ]
MALVAUX, P [1 ]
机构
[1] CATHOLIC UNIV LOUVAIN, DEPT PAEDIAT, B-1348 LOUVAIN LA NEUVE, BELGIUM
关键词
Growth; Parental height; Puberty; Turner syndrome;
D O I
10.1007/BF02106283
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Growth data on 100 patients with Turner syndrome are reported. Seventeen had spontaneous puberty. Between the ages 11 and 13 years, height and height velocity were higher in these girls than in those with induced puberty. Final adult height, however, was not different. Patients disomic for Xp chromosome were taller than the monosomic ones, and the majority of them had spontaneous puberty. Significant positive correlations were found between height of Turner syndrome patients and corrected mid parental height, mother's height and father's height from the age of 6 years. It is concluded that in patients with Turner syndrome spontaneous puberty and parental height should be accounted for in the evaluation of linear growth. © 1990 Springer-Verlag.
引用
收藏
页码:246 / 250
页数:5
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