RELATIONSHIP OF ALPHA-L-IDURONIDASE AND HURLER CORRECTIVE FACTOR

被引：43

作者：

SHAPIRO, LJ ^{[1
]}

HALL, CW ^{[1
]}

LEDER, IG ^{[1
]}

NEUFELD, EF ^{[1
]}

机构：

[1] NIAMDD,BETHESDA,MD 20014

来源：

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS | 1976年 / 172卷 / 01期

关键词：

D O I：

10.1016/0003-9861(76)90061-8

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

收藏

页码：156 / 161

页数：6

相关论文

共 23 条

[1] ADAIR WL, 1974, J BIOL CHEM, V249, P4696
[2] ASHWELL G, 1974, ADV ENZYMOL RAMB, V41, P99
[3] DEFECT IN HURLER AND SCHEIE SYNDROMES - DEFICIENCY OF ALPHA-IDURONIDASE
BACH, G
WEISSMAN.B
FRIEDMAN, R
NEUFELD, EF
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (08) : 2048 - &
[4] BARTON RW, 1971, J BIOL CHEM, V246, P7773
[5] A MODIFIED URONIC ACID CARBAZOLE REACTION
BITTER, T
MUIR, HM
[J]. ANALYTICAL BIOCHEMISTRY, 1962, 4 (04) : 330 - &
[6] IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
BROT, FE
GLASER, JH
ROOZEN, KJ
SLY, WS
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) : 1 - 8
[7] CANTZ M, 1972, METHOD ENZYMOL, V28, P884
[8] CIFONELLI JA, 1968, BIOCHEM PREP, V12, P12
[9] DEFECT IN HURLER AND HUNTER SYNDROMES, .2. DEFICIENCY OF SPECIFIC FACTORS INVOLVED IN MUCOPOLYSACCHARIDE DEGRADATION
FRATANTO.JC
HALL, CW
NEUFELD, EF
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 64 (01) : 360 - &
[10] PHENYL ALPHA-L-IDOPYRANOSIDURONIC AND BETA-L-IDOPYRANOSIDURONIC ACIDS AND SOME OTHER ARYL GLYCOPYRANOSIDURONIC ACIDS
FRIEDMAN, RB
WEISSMANN, B
[J]. CARBOHYDRATE RESEARCH, 1972, 24 (01) : 123 - +