BECKWITH-WIEDEMANN SYNDROME - DEVELOPMENT OF NEPHROBLASTOMA DURING THE SURVEILLANCE PERIOD

被引:19
作者
AZOUZ, EM [1 ]
LARSON, EJ [1 ]
PATEL, J [1 ]
GYEPES, MT [1 ]
机构
[1] EARL & LORAINE MILLER CHILDRENS HOSP,LONG BEACH,CA 90801
关键词
D O I
10.1007/BF02011388
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Two children, with Beckwith-Wiedemann syndrome and hemihypertrophy who were followed by ultrasonography, developed a large nephroblastoma in the interval between two abdominal ultrasound examinations. The customarily suggested bi-annual examinations are not frequent enough and may give physicians and parents a false sense of security. © 1990 Springer-Verlag.
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页码:550 / 552
页数:3
相关论文
共 12 条
[1]   PYELOCALYCEAL DIVERTICULA IN THE BECKWITH-WIEDEMANN SYNDROME [J].
BRONK, JB ;
PARKER, BR .
PEDIATRIC RADIOLOGY, 1987, 17 (01) :80-81
[2]  
GRUNER M, 1981, ANN RADIOL, V24, P39
[3]  
Jones KL, 1988, SMITHS RECOGNIZABLE
[4]  
LEBLANC A, 1979, ARCH FR PEDIATR, V36, P934
[5]  
LEE FA, 1972, RADIOL CLIN N AM, V10, P261
[6]  
MAROTEAUX P, 1982, MALADIES OSSEUSES EN
[7]   ASSOCIATION OF WILMSS TUMOR WITH ANIRIDIA HEMIHYPERTROPHY + OTHER CONGENITAL MALFORMATIONS [J].
MILLER, RW ;
MANNING, MD ;
FRAUMENI, JF .
NEW ENGLAND JOURNAL OF MEDICINE, 1964, 270 (18) :922-&
[8]  
PENDERGRASS TW, 1976, CANCER, V37, P403, DOI 10.1002/1097-0142(197601)37:1<403::AID-CNCR2820370152>3.0.CO
[9]  
2-H
[10]   BECKWITH-WIEDEMANN SYNDROME - ROLE OF ULTRASOUND IN ITS MANAGEMENT [J].
SHAH, KJ .
CLINICAL RADIOLOGY, 1983, 34 (03) :313-319