ABNORMAL COLLAGEN-METABOLISM IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH DUCHENNE MUSCULAR-DYSTROPHY

被引：41

作者：

RODEMANN, HP

BAYREUTHER, K

机构：

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1984年 / 81卷 / 16期

关键词：

D O I：

10.1073/pnas.81.16.5130

中图分类号：

Q [生物科学];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：5130 / 5134

页数：5

共 42 条

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[3] FIBROBLASTS DEGRADE NEWLY SYNTHESIZED COLLAGEN WITHIN CELL BEFORE SECRETION
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[J]. NATURE, 1978, 276 (5686) : 413 - 416
[4] DECREASE IN THE RATE OF PROTEIN-SYNTHESIS BY POLYSOMES FROM CULTURED FIBROBLASTS OF PATIENTS AND CARRIERS WITH DUCHENNE MUSCULAR-DYSTROPHY
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VANASSE, M
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[J]. CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES, 1979, 6 (03) : 355 - 358
[5] BUTTERFIELD DA, 1977, BIOCHIM BIOPHYS ACTA, V470, P1
[6] A ROLE FOR COLLAGEN IN THE PATHOGENESIS OF MUSCULAR-DYSTROPHY
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STEPHENS, HR
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BAILEY, AJ
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[J]. NATURE, 1980, 284 (5755) : 470 - 472
[7] DUBOWITZ V, 1978, MUSCLE DISORDERS CHI, P19
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[9] Fietzek P P, 1976, Int Rev Connect Tissue Res, V7, P1
[10] DECREASED LYSOSOMAL DIPEPTIDYL AMINOPEPTIDASE-I ACTIVITY IN CULTURED HUMAN-SKIN FIBROBLASTS IN DUCHENNES MUSCULAR-DYSTROPHY
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