CROW-FUKASE SYNDROME-ASSOCIATED WITH PULMONARY-HYPERTENSION

被引：26

作者：

IWASAKI, H

OGAWA, K

YOSHIDA, H

TAKASHIMA, F

SHIMIZU, K

LEE, JD

UEDA, T

NAKAMURA, T

机构：

[1] First Department of Internal Medicine, Fukui Medical School, Fukui

来源：

INTERNAL MEDICINE | 1993年 / 32卷 / 07期

关键词：

MYOCARDIAL HYPERTROPHY; ORGANOMEGALY; PLASMA CELL DYSCRASIA; MITOCHONDRIOSIS;

D O I：

10.2169/internalmedicine.32.556

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 60-year-old woman suffering from heart failure was found to have Crow-Fukase syndrome. A precise cardiovascular study revealed the existence of pulmonary hypertension (PH), cardiomegaly and myocardial hypertrophy in addition to manifestations of this syndrome such as hyperpigmentation, hypertrichosis, finger clubbing, polyneuropathy, organomegaly and plasma cell dyscrasia. These findings suggest the possibility that patients with Crow-Fukase syndrome have cardiopulmonary disorders including PH and cardiomegaly which might cause some cardiovascular symptoms such as peripheral edema and finger clubbing.

引用

页码：556 / 560

页数：5

共 15 条

[1]

Saikawa S., On the etiology “PEP syndrome (a peculiar progressive polyneuritis associated with pigmentation, edema, plasma cell dyscrasia), Med J, 32, (1980)

[2]

Bardwick P.A., Zvaifler N.J., Gill G.N., Newman D., Greenway G.D., Resnick D.L., Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: The POEMS syndromec-Report on two cases and a review of the literature, Medicine, 59, (1980)

[3]

Driedger H., Pruzanski W., Plasma cell neoplasia with peripheral polyneuropathy: A study of five cases and a review of the literature, Medicine, 59, (1980)

[4]

Nakanishi T., Sobue I., Toyokawa Y., Et al., The Crow-Fukase syndrome: A study of 102 cases in Japan, Neurology, 34, (1984)

[5]

Ohno R., Kimura K., Amaki I., Et al., Treatment of multiple myeloma with recombinant human leukocyte A interferon, Cancer Treat Rep, 69, (1985)

[6]

Sakakibara S., Konno S., Endomyocardial biopsy, Jpn Heart J, 3, (1962)

[7]

Iwasaki H., Ogawa K., Yoshida H., Et al., A case of Crow-Fukase syndrome associated with empty sella, Jpn Arch Internal Med, 36, (1989)

[8]

Takatsuki K., Sanada I., Plasma cell dyscrasia with polyneuropathy and endocrine disorder: clinical and laboratory features of 109 reported cases, Jpn J Clin Oncol, 13, (1983)

[9]

Inoue T., Ohta K., Ohhira H., Et al., Juvenile Crow-Fukase syndrome with response to bolus of methylprednisolone after failure of treatment by plasma exchange, Jpn J Clin Hematol, 31, (1990)

[10]

Shirabe S., Kishikawa M., Mine M., Miyazaki T., Kuratsune H., Tobinaga K., Crow-Fukase syndrome as sociated with extramedullary plasmacytoma, Jpn J Med, 30, (1991)

← 1 2 →