EARLY CLINICAL AND IMAGING (HIGH-FIELD MRI) DIAGNOSIS OF HALLERVORDEN-SPATZ DISEASE

被引:16
作者
FELICIANI, M [1 ]
CURATOLO, P [1 ]
机构
[1] UNIV ROMA LA SAPIENZA,INST PEDIAT NEUROL,DEPT NEUROL SCI,ROME,ITALY
关键词
HALLERVORDEN-SPATZ DISEASE; MAGNETIC RESONANCE IMAGING; IRON; GRADIENT-ECHO;
D O I
10.1007/BF00588145
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
In a 10-year-old girl, with progressive motor disturbance since the age of seven years and dominant pyramidal signs, MRI revealed marked overall low signal from the globus pallidus on each side, with central zones of high signal. There was also strikingly low signal in the zona reticularis of the substantia nigra, indicative of Hallervorden-Spatz disease (HSD).
引用
收藏
页码:247 / 248
页数:2
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