SURFACTANT PROTEIN-B DEFICIENCY - RADIOGRAPHIC MANIFESTATIONS

被引：12

作者：

HERMAN, TE

NOGEE, LM

MCALISTER, WH

DEHNER, LP

机构：

[1] JOHNS HOPKINS UNIV,SCH MED,DEPT PEDIAT,DIV NEONATOL,BALTIMORE,MD 21287

[2] WASHINGTON UNIV,SCH MED,ELIZABETH MALLINCKRODT DEPT PATHOL,ST LOUIS,MO 63110

来源：

PEDIATRIC RADIOLOGY | 1993年 / 23卷 / 05期

关键词：

D O I：

10.1007/BF02011963

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Surfactant is a complex structure primarily composed of phospholipids, but containing essential proteins as well. Congenital deficiency of Surfactant Protein-B (SPB) has recently been documented for the first time in two siblings. The pathologic findings in these infants was that of congenital pulmonary alveolar proteinosis and the radiographic manifestations were strikingly similar to hyaline membrane disease.

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页码：373 / 375

页数：3

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