SUCCESSFUL TREATMENT FOR A METASTATIC SUPRATENTORIAL MALIGNANT RHABDOID TUMOR

被引：10

作者：

BOUFFET, E

FRAPPAZ, D

DOLBEAU, D

SOBOL, H

JOUVET, A

CARRIE, C

PONDARRE, C

BRUNATMENTIGNY, M

PHILIP, T

MOTTOLESE, C

机构：

[1] CTR LEON BERARD, PATHOL UNIT, F-69373 LYON 08, FRANCE

[2] CTR LEON BERARD, ONCOL GENET UNIT, F-69373 LYON 08, FRANCE

[3] HOP WERTHEIMER, PATHOL UNIT, F-69003 LYON, FRANCE

[4] CTR LEON BERARD, RADIOTHERAPY UNIT, F-69373 LYON 08, FRANCE

[5] HOP WERTHEIMER, NEUROSURG UNIT, F-69003 LYON, FRANCE

来源：

JOURNAL OF NEURO-ONCOLOGY | 1993年 / 17卷 / 01期

关键词：

BRAIN; CHILDREN; RENDU-OSLER DISEASE; CHROMOSOME; 22; GENETIC; NEOPLASM; RHABDOID TUMOR;

D O I：

10.1007/BF01054275

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

The case of a boy with a familial history of Rendu-Osler disease, who successively developed a cerebellar pilocytic astrocytoma (at 3 years of age) and a metastatic supratentorial malignant rhabdoid tumor (at the age of 12 years) is reported. After a complete surgical removal, the CSF was cleared by 4 courses of chemotherapy, and the child received a craniospinal irradiation. He is currently alive and well 19 months after completion of the treatment. The authors discuss the ethiopathogeny of such intracranial tumors and argue for aggressive treatment.

引用

页码：65 / 70

页数：6

共 54 条

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