RESTRICTIVE CHEST BELLOWS DISEASE AND FRONTOMETAPHYSEAL DYSPLASIA

被引：6

作者：

LIPSON, E

AHMED, T

KIEL, MH

CHEDIAK, AD

机构：

[1] Sleep Disorders Center, Mt. Sinai Medical Center, Miami Beach

来源：

CHEST | 1993年 / 103卷 / 04期

关键词：

D O I：

10.1378/chest.103.4.1264

中图分类号：

R4 [临床医学];

学科分类号：

1002 ; 100602 ;

摘要：

We describe a patient with frontometaphyseal dysplasia (FMD), restrictive chest bellows disease, hypercapnic respiratory failure, and cor pulmonale. Treatment with intermittent supplemental oxygen, nocturnal nasal volume ventilation, and posture modification was successful in partial resolution of chronic hypoventilation and excessive daytime somnolence.

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收藏

页码：1264 / 1265

页数：2

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